Search Results

There are 27592 results for: content related to: Machado-Joseph disease gene product is a cytoplasmic protein widely expressed in brain

  1. You have free access to this content
    Down-regulation of heat shock protein 27 in neuronal cells and non-neuronal cells expressing mutant ataxin-3

    FEBS Letters

    Volume 546, Issue 2-3, July 10, 2003, Pages: 307–314, Feng-Chen Wen, Yen-Hsien Li, Hui-Fang Tsai, Chao-Hsiung Lin, Chuan Li, Chin-San Liu, Chong-Kuei Lii, Nobuyuki Nukina and Mingli Hsieh

    Version of Record online : 4 JUN 2003, DOI: 10.1016/S0014-5793(03)00605-7

  2. An Isoform of Ataxin-3 Accumulates in the Nucleus of Neuronal Cells in Affected Brain Regions of SCA3 Patients

    Brain Pathology

    Volume 8, Issue 4, October 1998, Pages: 669–679, Thorsten Schmidt, G. Bernhard Landwehrmeyer, Ina Schmitt, Yvon Trottier, Georg Auburger, Franco Laccone, Thomas Klockgether, Michael Völpel, Jörg T. Epplen, Ludger Schöls and Olaf Riess

    Version of Record online : 5 APR 2006, DOI: 10.1111/j.1750-3639.1998.tb00193.x

  3. You have free access to this content
    miR-25 alleviates polyQ-mediated cytotoxicity by silencing ATXN3

    FEBS Letters

    Volume 588, Issue 24, December 20, 2014, Pages: 4791–4798, Fengzhen Huang, Li Zhang, Zhe Long, Zhao Chen, Xuan Hou, Chunrong Wang, Huirong Peng, Junling Wang, Jiada Li, Ranhui Duan, Kun Xia, De-Maw Chuang, Beisha Tang and Hong Jiang

    Version of Record online : 20 NOV 2014, DOI: 10.1016/j.febslet.2014.11.013

  4. You have free access to this content
    Caspase-mediated proteolysis of the polyglutamine disease protein ataxin-3

    Journal of Neurochemistry

    Volume 89, Issue 4, May 2004, Pages: 908–918, Sarah J Shoesmith Berke, Francisca A Flores Schmied, Ewout R. Brunt, Lisa M. Ellerby and Henry L. Paulson

    Version of Record online : 8 APR 2004, DOI: 10.1111/j.1471-4159.2004.02369.x

  5. You have free access to this content
    Poster Presentations

    Movement Disorders

    Volume 27, Issue S1, June 2012, Pages: S1–S523,

    Version of Record online : 19 JUN 2012, DOI: 10.1002/mds.25051

  6. You have free access to this content
    p45, an ATPase subunit of the 19S proteasome, targets the polyglutamine disease protein ataxin-3 to the proteasome

    Journal of Neurochemistry

    Volume 101, Issue 6, June 2007, Pages: 1651–1661, Hongfeng Wang, Nali Jia, Erkang Fei, Zhiming Wang, Chao Liu, Tao Zhang, Jun Fan, Mian Wu, Lin Chen, Nobuyuki Nukina, Jiangning Zhou and Guanghui Wang

    Version of Record online : 22 JAN 2007, DOI: 10.1111/j.1471-4159.2007.04460.x

  7. Caffeine and adenosine A2A receptor inactivation decrease striatal neuropathology in a lentiviral-based model of Machado–Joseph disease

    Annals of Neurology

    Volume 73, Issue 5, May 2013, Pages: 655–666, Nélio Gonçalves, Ana T. Simões, Rodrigo A. Cunha and Luís Pereira de Almeida

    Version of Record online : 26 APR 2013, DOI: 10.1002/ana.23866

  8. You have free access to this content
    Structural and functional analysis of ataxin-2 and ataxin-3

    European Journal of Biochemistry

    Volume 271, Issue 15, August 2004, Pages: 3155–3170, Mario Albrecht, Michael Golatta, Ullrich Wüllner and Thomas Lengauer

    Version of Record online : 15 JUL 2004, DOI: 10.1111/j.1432-1033.2004.04245.x

  9. Novel candidate blood-based transcriptional biomarkers of machado-joseph disease

    Movement Disorders

    Volume 30, Issue 7, June 2015, Pages: 968–975, Mafalda Raposo, Conceição Bettencourt, Patrícia Maciel, Fuying Gao, Amanda Ramos, Nadiya Kazachkova, João Vasconcelos, Teresa Kay, Ana João Rodrigues, Bruno Bettencourt, Jácome Bruges-Armas, Daniel Geschwind, Giovanni Coppola and Manuela Lima

    Version of Record online : 25 APR 2015, DOI: 10.1002/mds.26238

  10. Prenatal diagnosis of Machado-Joseph disease/spinocerebellar ataxia type 3 in Taiwan: Early detection of expanded ataxin-3

    Journal of Clinical Laboratory Analysis

    Volume 17, Issue 5, 2003, Pages: 195–200, Hui-Fang Tsai, Chin-San Liu, Gin-Den Chen, Mei-Ling Lin, Chuan Li, Yi-Yun Chen, Bao-Tyan Wang and Mingli Hsieh

    Version of Record online : 18 AUG 2003, DOI: 10.1002/jcla.10092

  11. Structural modeling of ataxin-3 reveals distant homology to adaptins

    Proteins: Structure, Function, and Bioinformatics

    Volume 50, Issue 2, 1 February 2003, Pages: 355–370, Mario Albrecht, Daniel Hoffmann, Bernd O. Evert, Ina Schmitt, Ullrich Wüllner and Thomas Lengauer

    Version of Record online : 12 DEC 2002, DOI: 10.1002/prot.10280

  12. Decreased antioxidant enzyme activity and increased mitochondrial DNA damage in cellular models of Machado-Joseph disease

    Journal of Neuroscience Research

    Volume 87, Issue 8, June 2009, Pages: 1884–1891, Ya-Chun Yu, Chen-Ling Kuo, Wen-Ling Cheng, Chin-San Liu and Mingli Hsieh

    Version of Record online : 30 JAN 2009, DOI: 10.1002/jnr.22011

  13. Clinical and molecular events in patients with Machado–Joseph disease under lamotrigine therapy

    Acta Neurologica Scandinavica

    Volume 111, Issue 6, June 2005, Pages: 385–390, C.-S. Liu, H.-M. Hsu, W.-L. Cheng and M. Hsieh

    Version of Record online : 5 MAY 2005, DOI: 10.1111/j.1600-0404.2005.00405.x

  14. Abstracts of the inherited ataxias: A focus group meeting under the auspices of the Movement Disorder Society, Seattle, Washington, U.S.A., October 13–14, 1999

    Movement Disorders

    Volume 15, Issue 1, January 2000, Pages: 186–199,

    Version of Record online : 26 JAN 2001, DOI: 10.1002/1531-8257(200001)15:1<186::AID-MDS1038>3.0.CO;2-5

  15. Sequence-dependent and independent inhibition specific for mutant ataxin-3 by small interfering RNA

    Annals of Neurology

    Volume 56, Issue 1, July 2004, Pages: 124–129, Yi Li, Takanori Yokota, Ryusuke Matsumura, Kazunari Taira and Hidehiro Mizusawa

    Version of Record online : 28 JUN 2004, DOI: 10.1002/ana.20141

  16. Cerebral cortex involvement in Machado−Joseph disease

    European Journal of Neurology

    Volume 22, Issue 2, February 2015, Pages: 277–e24, T. J. R. de Rezende, A. D'Abreu, R. P. Guimarães, T. M. Lopes, I. Lopes-Cendes, F. Cendes, G. Castellano and M. C. França Jr

    Version of Record online : 23 SEP 2014, DOI: 10.1111/ene.12559

  17. You have free access to this content
    Domain architecture of the polyglutamine protein ataxin-3: a globular domain followed by a flexible tail

    FEBS Letters

    Volume 549, Issue 1-3, August 14, 2003, Pages: 21–25, Laura Masino, Valeria Musi, Rajesh P. Menon, Paola Fusi, Geoff Kelly, Thomas A. Frenkiel, Yvon Trottier and Annalisa Pastore

    Version of Record online : 22 JUL 2003, DOI: 10.1016/S0014-5793(03)00748-8

  18. Spinocerebellar Ataxias

    Neurodegeneration: The Molecular Pathology of Dementia and Movement Disorders, Second Edition

    Hidehiro Mizusawa, H. Brent Clark, Arnulf H. Koeppen, Pages: 273–287, 2011

    Published Online : 21 SEP 2011, DOI: 10.1002/9781444341256.ch27

  19. You have free access to this content
    Immunohistochemical study of neuronal intranuclear and cytoplasmic inclusions in Machado–Joseph disease

    Psychiatry and Clinical Neurosciences

    Volume 57, Issue 2, April 2003, Pages: 205–213, Masahiro Hayashi, Katsuji Kobayashi and Hisakazu Furuta

    Version of Record online : 23 SEP 2008, DOI: 10.1046/j.1440-1819.2003.01102.x

  20. The CAG/Polyglutamine Tract Diseases: Gene Products and Molecular Pathogenesis

    Brain Pathology

    Volume 7, Issue 3, July 1997, Pages: 927–942, Beena T. Koshy and Huda Y. Zoghbi

    Version of Record online : 28 JAN 2008, DOI: 10.1111/j.1750-3639.1997.tb00894.x