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There are 48995 results for: content related to: Sinus hypoplasia precedes sinus infection in a porcine model of cystic fibrosis

  1. You have free access to this content
    Disrupted posttranscriptional regulation of the cystic fibrosis transmembrane conductance regulator (CFTR) by a 5′UTR mutation is associated with a cftr-related disease

    Human Mutation

    Volume 32, Issue 10, October 2011, Pages: E2266–E2282, Samuel W. Lukowski, Cristina Bombieri and Ann E. O. Trezise

    Article first published online : 19 SEP 2011, DOI: 10.1002/humu.21545

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    Insertion of natural intron 6a-6b into a human cDNA-derived gene therapy vector for cystic fibrosis improves plasmid stability and permits facile RNA/DNA discrimination

    The Journal of Gene Medicine

    Volume 1, Issue 5, September/October 1999, Pages: 312–321, A. Christopher Boyd, Friedrich Popp, Uwe Michaelis, Heather Davidson, Hazel Davidson-Smith, Ann Doherty, Gerry McLachlan, David J. Porteous and Stefan Seeber

    Article first published online : 23 NOV 1999, DOI: 10.1002/(SICI)1521-2254(199909/10)1:5<312::AID-JGM55>3.0.CO;2-#

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    Altered ion transport by thyroid epithelia from CFTR−/− pigs suggests mechanisms for hypothyroidism in cystic fibrosis

    Experimental Physiology

    Volume 95, Issue 12, December 2010, Pages: 1132–1144, Hui Li, Suhasini Ganta and Peying Fong

    Article first published online : 20 SEP 2010, DOI: 10.1113/expphysiol.2010.054700

  4. You have full text access to this OnlineOpen article
    Abnormal tracheal smooth muscle function in the CF mouse

    Physiological Reports

    Volume 1, Issue 6, November 2013, Helen L. Wallace, Kevin W. Southern, Marilyn G. Connell, Susan Wray and Theodor Burdyga

    Article first published online : 5 NOV 2013, DOI: 10.1002/phy2.138

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    Endogenous surface expression of ΔF508-CFTR mediates cAMP-stimulated Cl current in CFTRΔF508/ΔF508 pig thyroid epithelial cells

    Experimental Physiology

    Volume 97, Issue 1, January 2012, Pages: 115–124, Yonghai Li, Suhasini Ganta and Peying Fong

    Article first published online : 20 OCT 2011, DOI: 10.1113/expphysiol.2011.060756

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    Congenital tracheal malformation in cystic fibrosis transmembrane conductance regulator-deficient mice

    The Journal of Physiology

    Volume 586, Issue 13, July 2008, Pages: 3231–3243, Elise Bonvin, Philippe Le Rouzic, Jean-François Bernaudin, Charles-Henry Cottart, Clarisse Vandebrouck, Antoine Crié, Teresinha Leal, Annick Clement and Monique Bonora

    Article first published online : 28 JUN 2008, DOI: 10.1113/jphysiol.2008.150763

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    Disruption of CFTR chloride channel alters mechanical properties and cAMP-dependent Cl transport of mouse aortic smooth muscle cells

    The Journal of Physiology

    Volume 568, Issue 2, October 2005, Pages: 483–495, Renaud Robert, Caroline Norez and Frédéric Becq

    Article first published online : 24 OCT 2005, DOI: 10.1113/jphysiol.2005.085019

  8. Cell therapy for cystic fibrosis

    Journal of Tissue Engineering and Regenerative Medicine

    Sean V. Murphy and Anthony Atala

    Article first published online : 25 JUL 2013, DOI: 10.1002/term.1746

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    Cftr and ENaC ion channels mediate NaCl absorption in the mouse submandibular gland

    The Journal of Physiology

    Volume 588, Issue 4, February 2010, Pages: 713–724, Marcelo A. Catalán, Tetsuji Nakamoto, Mireya Gonzalez-Begne, Jean M. Camden, Susan M. Wall, Lane L. Clarke and James E. Melvin

    Article first published online : 12 FEB 2010, DOI: 10.1113/jphysiol.2009.183541

  10. Common CFTR haplotypes and susceptibility to chronic pancreatitis and congenital bilateral absence of the vas deferens

    Human Mutation

    Volume 32, Issue 8, August 2011, Pages: 912–920, Bernhard Steiner, Jonas Rosendahl, Heiko Witt, Niels Teich, Volker Keim, Hans-Ulrich Schulz, Roland Pfützer, Matthias Lühr, Thomas M. Gress, Renate Nickel, Olfert Landt, Monika Koudova, Milan Macek Jr, Antoni Farre, Teresa Casals, Marie-Claire Desax, Sabina Gallati, Macarena Gomez-Lira, Marie Pierre Audrezet, Claude Férec, Marie des Georges, Mireille Claustres and Kaspar Truninger

    Article first published online : 7 JUN 2011, DOI: 10.1002/humu.21511

  11. You have full text access to this Open Access content
    Molecular mechanisms controlling CFTR gene expression in the airway

    Journal of Cellular and Molecular Medicine

    Volume 16, Issue 6, June 2012, Pages: 1321–1330, Zhaolin Zhang, Christopher J. Ott, Marzena A. Lewandowska, Shih-Hsing Leir and Ann Harris

    Article first published online : 28 MAY 2012, DOI: 10.1111/j.1582-4934.2011.01439.x

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    Genetic Investigations of CFTR Mutations in Congenital Absence of Vas Deferens, Uterus, and Vagina as a Cause of Infertility

    Journal of Andrology

    Volume 29, Issue 5, September-October 2008, Pages: 506–513, Ramin Radpour, Hamid Gourabi, Ahmad Vosough Dizaj, Wolfgang Holzgreve and Xiao Yan Zhong

    Article first published online : 2 JAN 2013, DOI: 10.2164/jandrol.108.005074

  13. CFTR mutations and polymorphisms in male infertility

    International Journal of Andrology

    Volume 27, Issue 5, October 2004, Pages: 251–256, Harry Cuppens and Jean-Jacques Cassiman

    Article first published online : 17 SEP 2004, DOI: 10.1111/j.1365-2605.2004.00485.x

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    The Phenotypic Consequences of CFTR Mutations

    Annals of Human Genetics

    Volume 67, Issue 5, September 2003, Pages: 471–485, Rebecca K. Rowntree and Ann Harris

    Article first published online : 27 AUG 2003, DOI: 10.1046/j.1469-1809.2003.00028.x

  15. You have full text access to this Open Access content
    A complex intronic enhancer regulates expression of the CFTR gene by direct interaction with the promoter

    Journal of Cellular and Molecular Medicine

    Volume 13, Issue 4, April 2009, Pages: 680–692, Christopher J. Ott, Magdalena Suszko, Neil P. Blackledge, Jane E. Wright, Gregory E. Crawford and Ann Harris

    Article first published online : 24 DEC 2008, DOI: 10.1111/j.1582-4934.2008.00621.x

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    Analysis of a DNase I hypersensitive site located −20.9 kb upstream of the CFTR gene

    European Journal of Biochemistry

    Volume 266, Issue 2, December 1999, Pages: 431–443, Hugh N. Nuthall, Georges Vassaux, Clare Huxley and Ann Harris

    Article first published online : 25 DEC 2001, DOI: 10.1046/j.1432-1327.1999.00872.x

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    Complementation of null CF mice with a human CFTR YAC transgene

    The EMBO Journal

    Volume 16, Issue 14, July 15, 1997, Pages: 4238–4249, Ania L. Manson, Ann E. O. Trezise, Lesley J. MacVinish, Kristin D. Kasschau, Nina Birchall, Vasso Episkopou, Georges Vassaux, Martin J. Evans, William H. Colledge, Alan W. Cuthbert and Clare Huxley

    Article first published online : 15 JUL 1997, DOI: 10.1093/emboj/16.14.4238

  18. CFTR: The CF Gene and Its Regulation in Physiology and Disease

    Standard Article

    eLS

    Wayne IL Davies

    Published Online : 8 DEC 2013, DOI: 10.1002/9780470015902.a0022929

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    UMD-CFTR: A database dedicated to CF and CFTR-related disorders

    Human Mutation

    Volume 31, Issue 9, September 2010, Pages: 1011–1019, Corinne Bareil, Corinne Thèze, Christophe Béroud, Dalil Hamroun, Caroline Guittard, Céline René, Damien Paulet, Marie des Georges and Mireille Claustres

    Article first published online : 6 JUL 2010, DOI: 10.1002/humu.21316

  20. You have free access to this content
    Evaluation of potential regulatory elements identified as DNase I hypersensitive sites in the CFTR gene

    European Journal of Biochemistry

    Volume 269, Issue 2, January 2002, Pages: 553–559, Marios Phylactides, Rebecca Rowntree, Hugh Nuthall, David Ussery, Ann Wheeler and Ann Harris

    Article first published online : 22 FEB 2002, DOI: 10.1046/j.0014-2956.2001.02679.x