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There are 3179268 results for: content related to: Serum insulin-like system alterations in patients with spinocerebellar ataxia type 3

  1. Degeneration of the central vestibular system in spinocerebellar ataxia type 3 (SCA3) patients and its possible clinical significance

    Neuropathology and Applied Neurobiology

    Volume 30, Issue 4, August 2004, Pages: 402–414, U. Rüb, E. R. Brunt, R. A. I. De Vos, D. Del Turco, K. Del Tredici, K. Gierga, C. Schultz, E. Ghebremedhin, K. Bürk, G. Auburger and H. Braak

    Article first published online : 4 MAY 2004, DOI: 10.1111/j.1365-2990.2004.00554.x

  2. Spinocerebellar Ataxia Type 3 (SCA3): Thalamic Neurodegeneration Occurs Independently from Thalamic Ataxin-3 Immunopositive Neuronal Intranuclear Inclusions

    Brain Pathology

    Volume 16, Issue 3, July 2006, Pages: 218–227, Udo Rüb, Rob A.I. De Vos, Ewout R. Brunt, Tamás Sebestény, Ludger Schöls, Georg Auburger, Jürgen Bohl, Estifanos Ghebremedhin, Kristin Gierga, Kay Seidel, Wilfred Den Dunnen, Helmut Heinsen, Henry Paulson and Thomas Deller

    Article first published online : 4 AUG 2006, DOI: 10.1111/j.1750-3639.2006.00022.x

  3. Schwann cell involvement in the peripheral neuropathy of spinocerebellar ataxia type 3

    Neuropathology and Applied Neurobiology

    Volume 40, Issue 5, August 2014, Pages: 628–639, Noriaki Suga, Masahisa Katsuno, Haruki Koike, Haruhiko Banno, Keisuke Suzuki, Atsushi Hashizume, Tomoo Mano, Masahiro Iijima, Yuichi Kawagashira, Masaaki Hirayama, Tomohiko Nakamura, Hirohisa Watanabe, Fumiaki Tanaka and Gen Sobue

    Article first published online : 1 JUL 2014, DOI: 10.1111/nan.12055

  4. Cellular protein quality control and the evolution of aggregates in spinocerebellar ataxia type 3 (SCA3)

    Neuropathology and Applied Neurobiology

    Volume 38, Issue 6, October 2012, Pages: 548–558, K. Seidel, M. Meister, G. J. Dugbartey, M. P. Zijlstra, J. Vinet, E. R. P. Brunt, F. W. van Leeuwen, U. Rüb, H. H. Kampinga and W. F. A. den Dunnen

    Article first published online : 17 SEP 2012, DOI: 10.1111/j.1365-2990.2011.01220.x

  5. Autosomal dominant cerebellar ataxia: Phenotypic differences in genetically defined subtypes?

    Annals of Neurology

    Volume 42, Issue 6, December 1997, Pages: 924–932, Dr. Ludger Schöls, Georgios Amoiridis, Thomas Büttner, Horst Przuntek, Jörg T. Epplen and Olaf Riess

    Article first published online : 8 OCT 2004, DOI: 10.1002/ana.410420615

  6. Protein surveillance machinery in brains with spinocerebellar ataxia type 3: Redistribution and differential recruitment of 26S proteasome subunits and chaperones to neuronal intranuclear inclusions

    Annals of Neurology

    Volume 51, Issue 3, March 2002, Pages: 302–310, Thorsten Schmidt, Katrin S. Lindenberg, Antje Krebs, Ludger Schöls, Franco Laccone, Jochen Herms, Martin Rechsteiner, Olaf Riess and G. Bernhard Landwehrmeyer

    Article first published online : 27 FEB 2002, DOI: 10.1002/ana.10101

  7. Degeneration of ingestion-related brainstem nuclei in spinocerebellar ataxia type 2, 3, 6 and 7

    Neuropathology and Applied Neurobiology

    Volume 32, Issue 6, December 2006, Pages: 635–649, U. Rüb, E. R. Brunt, E. Petrasch-Parwez, L. Schöls, D. Theegarten, G. Auburger, K. Seidel, C. Schultz, K. Gierga, H. Paulson, C. Van Broeckhoven, T. Deller and R. A. I. De Vos

    Article first published online : 8 AUG 2006, DOI: 10.1111/j.1365-2990.2006.00772.x

  8. Lack of mutations in spinocerebellar ataxia type 2 and 3 genes in a Taiwanese (ethnic Chinese) cohort of familial and early-onset parkinsonism

    American Journal of Medical Genetics Part B: Neuropsychiatric Genetics

    Volume 144B, Issue 4, 5 June 2007, Pages: 434–438, Chin-Hsien Lin, Wuh-Liang Hwu, Shu-Chuan Chiang, Chun-Hwei Tai and Ruey-Meei Wu

    Article first published online : 17 APR 2007, DOI: 10.1002/ajmg.b.30427

  9. An Isoform of Ataxin-3 Accumulates in the Nucleus of Neuronal Cells in Affected Brain Regions of SCA3 Patients

    Brain Pathology

    Volume 8, Issue 4, October 1998, Pages: 669–679, Thorsten Schmidt, G. Bernhard Landwehrmeyer, Ina Schmitt, Yvon Trottier, Georg Auburger, Franco Laccone, Thomas Klockgether, Michael Völpel, Jörg T. Epplen, Ludger Schöls and Olaf Riess

    Article first published online : 5 APR 2006, DOI: 10.1111/j.1750-3639.1998.tb00193.x

  10. Levels of DNAJB family members (HSP40) correlate with disease onset in patients with spinocerebellar ataxia type 3

    European Journal of Neuroscience

    Volume 32, Issue 5, September 2010, Pages: 760–770, M. P. Zijlstra, M. A. Rujano, M. A. Van Waarde, E. Vis, E. R. Brunt and H. H. Kampinga

    Article first published online : 19 AUG 2010, DOI: 10.1111/j.1460-9568.2010.07352.x

  11. Progressive cognitive dysfunction in spinocerebellar ataxia type 3

    Movement Disorders

    Volume 28, Issue 10, September 2013, Pages: 1435–1438, Sandra Roeske, Ina Filla, Stefan Heim, Katrin Amunts, Christoph Helmstaedter, Ullrich Wüllner, Michael Wagner, Thomas Klockgether and Martina Minnerop

    Article first published online : 4 JUN 2013, DOI: 10.1002/mds.25512

  12. Sleep in other Neurodegenerative Diseases

    Sleep Disorders in Neurology: A Practical Approach

    Sebastiaan Overeem, Paul Reading, Pages: 124–135, 2010

    Published Online : 30 APR 2010, DOI: 10.1002/9781444315158.ch11

  13. Variation of CAG repeats and two intragenic polymorphisms at SCA3 locus among Machado–Joseph disease/SCA3 patients and diverse normal populations from eastern India

    Acta Neurologica Scandinavica

    Volume 108, Issue 6, December 2003, Pages: 407–414, B. Chattopadhyay, P. Basu, P. K. Gangopadhyay, S. C. Mukherjee, K. K. Sinha, A. Chakraborty, T. Roy, S. Roychoudhury, P. P. Majumder and N. P. Bhattacharyya

    Article first published online : 22 SEP 2003, DOI: 10.1034/j.1600-0404.2003.00167.x

  14. Spinocerebellar ataxia 3 and machado-joseph disease: Clinical, molecular, and neuropathological features

    Annals of Neurology

    Volume 39, Issue 4, April 1996, Pages: 490–499, Dr Alexandra Durr, Giovanni Stevanin, Geraldine Cancel, Charles Duyckaerts, Nacer Abbas, Olivier Didierjean, Herve Chneiweiss, Ali Benomar, Olivier Lyon-Caen, Jean Julien, Michel Serdaru, Christiane Penet, Yves Agid and Alexis Brice

    Article first published online : 8 OCT 2004, DOI: 10.1002/ana.410390411

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    Poster Presentations

    Movement Disorders

    Volume 27, Issue S1, June 2012, Pages: S1–S523,

    Article first published online : 19 JUN 2012, DOI: 10.1002/mds.25051

  16. Absence of spinocerebellar ataxia type 3/Machado–Joseph disease within ataxic patients in the Czech population

    European Journal of Neurology

    Volume 12, Issue 11, November 2005, Pages: 851–857, P. O. Bauer, A. Zumrova, V. Matoska, T. Marikova, S. Krilova, A. Boday, B. Singh and P. Goetz

    Article first published online : 20 OCT 2005, DOI: 10.1111/j.1468-1331.2005.01090.x

  17. You have free access to this content
    Neocortical Atrophy in Machado-Joseph Disease: A Longitudinal Neuroimaging Study

    Journal of Neuroimaging

    Volume 22, Issue 3, July 2012, Pages: 285–291, Anelyssa D’Abreu, Marcondes C. França Jr., Clarissa L. Yasuda, Bruno A. G. Campos, Iscia Lopes-Cendes and Fernando Cendes

    Article first published online : 23 JUN 2011, DOI: 10.1111/j.1552-6569.2011.00614.x

  18. Motor evoked potentials in the spinocerebellar ataxias type 1 and type 3

    Muscle & Nerve

    Volume 20, Issue 2, February 1997, Pages: 226–228, Ludger Schöls, Georgios Amoiridis, Mathias Langkafel, Stephan Schöls and Horst Przuntek

    Article first published online : 7 DEC 1998, DOI: 10.1002/(SICI)1097-4598(199702)20:2<226::AID-MUS14>3.0.CO;2-0

  19. Guidelines for the pathoanatomical examination of the lower brain stem in ingestive and swallowing disorders and its application to a dysphagic spinocerebellar ataxia type 3 patient

    Neuropathology and Applied Neurobiology

    Volume 29, Issue 1, February 2003, Pages: 1–13, U. Rüb, E. R. Brunt, D. Del Turco, R. A. I. De Vos, K. Gierga, H. Paulson and H. Braak

    Article first published online : 11 FEB 2003, DOI: 10.1046/j.1365-2990.2003.00437.x

  20. Somatic mosaicism of the CAG repeat expansion in spinocerebellar ataxia type 3/Machado-Joseph disease

    Human Mutation

    Volume 11, Issue 1, 1998, Pages: 23–27, Géraldine Cancel, Isabelle Gourfinkel-An, Giovanni Stevanin, Olivier Didierjean, Nacer Abbas, Etienne Hirsch, Yves Agid and Alexis Brice

    Article first published online : 7 JAN 1999, DOI: 10.1002/(SICI)1098-1004(1998)11:1<23::AID-HUMU4>3.0.CO;2-M