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There are 2813 results for: content related to: Progressive cognitive dysfunction in spinocerebellar ataxia type 3

  1. Spinocerebellar Ataxia Type 3 (SCA3): Thalamic Neurodegeneration Occurs Independently from Thalamic Ataxin-3 Immunopositive Neuronal Intranuclear Inclusions

    Brain Pathology

    Volume 16, Issue 3, July 2006, Pages: 218–227, Udo Rüb, Rob A.I. De Vos, Ewout R. Brunt, Tamás Sebestény, Ludger Schöls, Georg Auburger, Jürgen Bohl, Estifanos Ghebremedhin, Kristin Gierga, Kay Seidel, Wilfred Den Dunnen, Helmut Heinsen, Henry Paulson and Thomas Deller

    Version of Record online : 4 AUG 2006, DOI: 10.1111/j.1750-3639.2006.00022.x

  2. Degeneration of the central vestibular system in spinocerebellar ataxia type 3 (SCA3) patients and its possible clinical significance

    Neuropathology and Applied Neurobiology

    Volume 30, Issue 4, August 2004, Pages: 402–414, U. Rüb, E. R. Brunt, R. A. I. De Vos, D. Del Turco, K. Del Tredici, K. Gierga, C. Schultz, E. Ghebremedhin, K. Bürk, G. Auburger and H. Braak

    Version of Record online : 4 MAY 2004, DOI: 10.1111/j.1365-2990.2004.00554.x

  3. Oculomotor deficits in spinocerebellar ataxia type 3: Potential biomarkers of preclinical detection and disease progression

    CNS Neuroscience & Therapeutics

    Volume 23, Issue 4, April 2017, Pages: 321–328, Chao Wu, Ding-Bang Chen, Li Feng, Xiang-Xue Zhou, Ji-Wei Zhang, Hua-Jing You, Xiu-Ling Liang, Zhong Pei and Xun-Hua Li

    Version of Record online : 13 FEB 2017, DOI: 10.1111/cns.12676

  4. Degeneration of ingestion-related brainstem nuclei in spinocerebellar ataxia type 2, 3, 6 and 7

    Neuropathology and Applied Neurobiology

    Volume 32, Issue 6, December 2006, Pages: 635–649, U. Rüb, E. R. Brunt, E. Petrasch-Parwez, L. Schöls, D. Theegarten, G. Auburger, K. Seidel, C. Schultz, K. Gierga, H. Paulson, C. Van Broeckhoven, T. Deller and R. A. I. De Vos

    Version of Record online : 8 AUG 2006, DOI: 10.1111/j.1365-2990.2006.00772.x

  5. Parametric fMRI of paced motor responses uncovers novel whole-brain imaging biomarkers in spinocerebellar ataxia type 3

    Human Brain Mapping

    Volume 37, Issue 10, October 2016, Pages: 3656–3668, João Valente Duarte, Ricardo Faustino, Mercês Lobo, Gil Cunha, César Nunes, Carlos Ferreira, Cristina Januário and Miguel Castelo-Branco

    Version of Record online : 7 JUN 2016, DOI: 10.1002/hbm.23266

  6. Schwann cell involvement in the peripheral neuropathy of spinocerebellar ataxia type 3

    Neuropathology and Applied Neurobiology

    Volume 40, Issue 5, August 2014, Pages: 628–639, Noriaki Suga, Masahisa Katsuno, Haruki Koike, Haruhiko Banno, Keisuke Suzuki, Atsushi Hashizume, Tomoo Mano, Masahiro Iijima, Yuichi Kawagashira, Masaaki Hirayama, Tomohiko Nakamura, Hirohisa Watanabe, Fumiaki Tanaka and Gen Sobue

    Version of Record online : 1 JUL 2014, DOI: 10.1111/nan.12055

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    CDK5 protects from caspase-induced Ataxin-3 cleavage and neurodegeneration

    Journal of Neurochemistry

    Volume 129, Issue 6, June 2014, Pages: 1013–1023, Jan Liman, Sebastian Deeg, Aaron Voigt, Hannes Voßfeldt, Christoph P. Dohm, André Karch, Jochen Weishaupt, Jörg B. Schulz, Mathias Bähr and Pawel Kermer

    Version of Record online : 24 MAR 2014, DOI: 10.1111/jnc.12684

  8. You have free access to this content
    Poster Presentations

    Movement Disorders

    Volume 29, Issue S1, May 2014, Pages: S1–S571,

    Version of Record online : 6 JUN 2014, DOI: 10.1002/mds.25914

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    miR-25 alleviates polyQ-mediated cytotoxicity by silencing ATXN3

    FEBS Letters

    Volume 588, Issue 24, December 20, 2014, Pages: 4791–4798, Fengzhen Huang, Li Zhang, Zhe Long, Zhao Chen, Xuan Hou, Chunrong Wang, Huirong Peng, Junling Wang, Jiada Li, Ranhui Duan, Kun Xia, De-Maw Chuang, Beisha Tang and Hong Jiang

    Version of Record online : 20 NOV 2014, DOI: 10.1016/j.febslet.2014.11.013

  10. Involvement of the auditory brainstem system in spinocerebellar ataxia type 2 (SCA2), type 3 (SCA3) and type 7 (SCA7)

    Neuropathology and Applied Neurobiology

    Volume 34, Issue 5, October 2008, Pages: 479–491, F. Hoche, K. Seidel, E. R. Brunt, G. Auburger, L. Schöls, K. Bürk, R. A. De Vos, W. Den Dunnen, I. Bechmann, R. Egensperger, C. Van Broeckhoven, K. Gierga, T. Deller and U. Rüb

    Version of Record online : 24 JAN 2008, DOI: 10.1111/j.1365-2990.2007.00933.x

  11. Levels of DNAJB family members (HSP40) correlate with disease onset in patients with spinocerebellar ataxia type 3

    European Journal of Neuroscience

    Volume 32, Issue 5, September 2010, Pages: 760–770, M. P. Zijlstra, M. A. Rujano, M. A. Van Waarde, E. Vis, E. R. Brunt and H. H. Kampinga

    Version of Record online : 19 AUG 2010, DOI: 10.1111/j.1460-9568.2010.07352.x

  12. On the distribution of intranuclear and cytoplasmic aggregates in the brainstem of patients with spinocerebellar ataxia type 2 and 3

    Brain Pathology

    Volume 27, Issue 3, May 2017, Pages: 345–355, Kay Seidel, Sonny Siswanto, Michaela Fredrich, Mohamed Bouzrou, Wilfred F.A. den Dunnen, Inci Özerden, Horst-Werner Korf, Bela Melegh, Jeroen J. de Vries, Ewout R. Brunt, Georg Auburger and Udo Rüb

    Version of Record online : 2 AUG 2016, DOI: 10.1111/bpa.12412

  13. Lack of mutations in spinocerebellar ataxia type 2 and 3 genes in a Taiwanese (ethnic Chinese) cohort of familial and early-onset parkinsonism

    American Journal of Medical Genetics Part B: Neuropsychiatric Genetics

    Volume 144B, Issue 4, 5 June 2007, Pages: 434–438, Chin-Hsien Lin, Wuh-Liang Hwu, Shu-Chuan Chiang, Chun-Hwei Tai and Ruey-Meei Wu

    Version of Record online : 17 APR 2007, DOI: 10.1002/ajmg.b.30427

  14. Absence of spinocerebellar ataxia type 3/Machado–Joseph disease within ataxic patients in the Czech population

    European Journal of Neurology

    Volume 12, Issue 11, November 2005, Pages: 851–857, P. O. Bauer, A. Zumrova, V. Matoska, T. Marikova, S. Krilova, A. Boday, B. Singh and P. Goetz

    Version of Record online : 20 OCT 2005, DOI: 10.1111/j.1468-1331.2005.01090.x

  15. Variation of CAG repeats and two intragenic polymorphisms at SCA3 locus among Machado–Joseph disease/SCA3 patients and diverse normal populations from eastern India

    Acta Neurologica Scandinavica

    Volume 108, Issue 6, December 2003, Pages: 407–414, B. Chattopadhyay, P. Basu, P. K. Gangopadhyay, S. C. Mukherjee, K. K. Sinha, A. Chakraborty, T. Roy, S. Roychoudhury, P. P. Majumder and N. P. Bhattacharyya

    Version of Record online : 22 SEP 2003, DOI: 10.1034/j.1600-0404.2003.00167.x

  16. Protein surveillance machinery in brains with spinocerebellar ataxia type 3: Redistribution and differential recruitment of 26S proteasome subunits and chaperones to neuronal intranuclear inclusions

    Annals of Neurology

    Volume 51, Issue 3, March 2002, Pages: 302–310, Thorsten Schmidt, Katrin S. Lindenberg, Antje Krebs, Ludger Schöls, Franco Laccone, Jochen Herms, Martin Rechsteiner, Olaf Riess and G. Bernhard Landwehrmeyer

    Version of Record online : 27 FEB 2002, DOI: 10.1002/ana.10101

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    Abstracts

    Movement Disorders

    Volume 32, Issue S2, June 2017, Pages: S1–S627,

    Version of Record online : 2 JUN 2017, DOI: 10.1002/mds.27087

  18. Cerebral cortex involvement in Machado−Joseph disease

    European Journal of Neurology

    Volume 22, Issue 2, February 2015, Pages: 277–e24, T. J. R. de Rezende, A. D'Abreu, R. P. Guimarães, T. M. Lopes, I. Lopes-Cendes, F. Cendes, G. Castellano and M. C. França Jr

    Version of Record online : 23 SEP 2014, DOI: 10.1111/ene.12559

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    Poster Presentations

    Movement Disorders

    Volume 27, Issue S1, June 2012, Pages: S1–S523,

    Version of Record online : 19 JUN 2012, DOI: 10.1002/mds.25051

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    Poster Session

    Movement Disorders

    Volume 31, Issue S2, June 2016, Pages: S1–S697,

    Version of Record online : 19 JUN 2016, DOI: 10.1002/mds.26688