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There are 9992 results for: content related to: RNA quality control and protein aggregates in amyotrophic lateral sclerosis: A review

  1. Genetic heterogeneity of amyotrophic lateral sclerosis: Implications for clinical practice and research

    Muscle & Nerve

    Volume 49, Issue 6, June 2014, Pages: 786–803, Xiaowei W. Su, James R. Broach, James R. Connor, Glenn S. Gerhard and Zachary Simmons

    Version of Record online : 8 APR 2014, DOI: 10.1002/mus.24198

  2. Review: Transactive response DNA-binding protein 43 (TDP-43): mechanisms of neurodegeneration

    Neuropathology and Applied Neurobiology

    Volume 36, Issue 2, April 2010, Pages: 97–112, T. F. Gendron, K. A. Josephs and L. Petrucelli

    Version of Record online : 23 MAR 2010, DOI: 10.1111/j.1365-2990.2010.01060.x

  3. You have full text access to this OnlineOpen article
    Spliceosome integrity is defective in the motor neuron diseases ALS and SMA

    EMBO Molecular Medicine

    Volume 5, Issue 2, February 2013, Pages: 221–234, Hitomi Tsuiji, Yohei Iguchi, Asako Furuya, Ayane Kataoka, Hiroyuki Hatsuta, Naoki Atsuta, Fumiaki Tanaka, Yoshio Hashizume, Hiroyasu Akatsu, Shigeo Murayama, Gen Sobue and Koji Yamanaka

    Version of Record online : 25 JAN 2013, DOI: 10.1002/emmm.201202303

  4. TARDBP and FUS Mutations Associated with Amyotrophic Lateral Sclerosis: Summary and Update

    Human Mutation

    Volume 34, Issue 6, June 2013, Pages: 812–826, Serena Lattante, Guy A. Rouleau and Edor Kabashi

    Version of Record online : 29 APR 2013, DOI: 10.1002/humu.22319

  5. RNA-binding proteins in neurodegenerative disease: TDP-43 and beyond

    Wiley Interdisciplinary Reviews: RNA

    Volume 3, Issue 2, March/April 2012, Pages: 265–285, Keith A. Hanson, Sang Hwa Kim and Randal S. Tibbetts

    Version of Record online : 25 OCT 2011, DOI: 10.1002/wrna.111

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    TDP-43 and FUS/TLS: cellular functions and implications for neurodegeneration

    The FEBS Journal

    Volume 278, Issue 19, October 2011, Pages: 3550–3568, Fabienne C. Fiesel and Philipp J. Kahle

    Version of Record online : 24 AUG 2011, DOI: 10.1111/j.1742-4658.2011.08258.x

  7. TDP-43 loss of function increases TFEB activity and blocks autophagosome–lysosome fusion

    The EMBO Journal

    Volume 35, Issue 2, 18 January 2016, Pages: 121–142, Qin Xia, Hongfeng Wang, Zongbing Hao, Cheng Fu, Qingsong Hu, Feng Gao, Haigang Ren, Dong Chen, Junhai Han, Zheng Ying and Guanghui Wang

    Version of Record online : 23 DEC 2015, DOI: 10.15252/embj.201591998

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    Physiological Functions and Pathobiology of TDP-43 and FUS/TLS proteins

    Journal of Neurochemistry

    Accepted manuscript online: 26 MAR 2016, Antonia Ratti and Emanuele Buratti

    DOI: 10.1111/jnc.13625

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    What is the key player in TDP-43 pathology in ALS: Disappearance from the nucleus or inclusion formation in the cytoplasm?

    Neurology and Clinical Neuroscience

    Volume 1, Issue 1, January 2013, Pages: 11–17, Osamu Onodera, Akihiro Sugai, Takuya Konno, Mari Tada, Akihide Koyama and Masatoyo Nishizawa

    Version of Record online : 31 JAN 2013, DOI: 10.1002/ncn3.9

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    TDP-43 and FUS/TLS: sending a complex message about messenger RNA in amyotrophic lateral sclerosis?

    The FEBS Journal

    Volume 278, Issue 19, October 2011, Pages: 3569–3577, Michael J. Strong and Kathryn Volkening

    Version of Record online : 6 SEP 2011, DOI: 10.1111/j.1742-4658.2011.08277.x

  11. Cytoplasmic TDP-43 accumulation in cells of the adrenal medulla in individuals with or without amyotrophic lateral sclerosis

    Neuropathology

    Volume 34, Issue 6, December 2014, Pages: 535–540, Koichi Okamoto, Masakuni Amari, Yukio Fujita, Kouki Makioka, Toshio Fukuda, Keiji Suzuki and Masamitsu Takatama

    Version of Record online : 11 JUL 2014, DOI: 10.1111/neup.12139

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    Adenoviral expression of TDP-43 and FUS genes and shRNAs for protein degradation pathways in rodent motoneurons in vitro and in vivo

    Neuropathology

    Volume 34, Issue 1, February 2014, Pages: 83–98, Kazuhiko Watabe, Keiko Akiyama, Emiko Kawakami, Tomohiro Ishii, Kentaro Endo, Hiroko Yanagisawa, Kazunori Sango and Masami Tsukamoto

    Version of Record online : 12 AUG 2013, DOI: 10.1111/neup.12058

  13. An MND/ALS phenotype associated with C9orf72 repeat expansion: Abundant p62-positive, TDP-43-negative inclusions in cerebral cortex, hippocampus and cerebellum but without associated cognitive decline

    Neuropathology

    Volume 32, Issue 5, October 2012, Pages: 505–514, Claire Troakes, Satomi Maekawa, Lokesh Wijesekera, Boris Rogelj, László Siklós, Christopher Bell, Bradley Smith, Stephen Newhouse, Caroline Vance, Lauren Johnson, Tibor Hortobágyi, Aleksey Shatunov, Ammar Al-Chalabi, Nigel Leigh, Christopher E. Shaw, Andrew King and Safa Al-Sarraj

    Version of Record online : 19 DEC 2011, DOI: 10.1111/j.1440-1789.2011.01286.x

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    Knockdown of transactive response DNA-binding protein (TDP-43) downregulates histone deacetylase 6

    The EMBO Journal

    Volume 29, Issue 1, January 6, 2010, Pages: 209–221, Fabienne C Fiesel, Aaron Voigt, Stephanie S Weber, Chris Van den Haute, Andrea Waldenmaier, Karin Görner, Michael Walter, Marlene L Anderson, Jeannine V Kern, Tobias M Rasse, Thorsten Schmidt, Wolfdieter Springer, Roland Kirchner, Michael Bonin, Manuela Neumann, Veerle Baekelandt, Marianna Alunni-Fabbroni, Jörg B Schulz and Philipp J Kahle

    Version of Record online : 12 NOV 2009, DOI: 10.1038/emboj.2009.324

  15. You have full text access to this OnlineOpen article
    Review: Prion-like mechanisms of transactive response DNA binding protein of 43 kDa (TDP-43) in amyotrophic lateral sclerosis (ALS)

    Neuropathology and Applied Neurobiology

    Volume 41, Issue 5, August 2015, Pages: 578–597, Phillip Smethurst, Katie Claire Louise Sidle and John Hardy

    Version of Record online : 20 APR 2015, DOI: 10.1111/nan.12206

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    XBP1 depletion precedes ubiquitin aggregation and Golgi fragmentation in TDP-43 transgenic rats

    Journal of Neurochemistry

    Volume 123, Issue 3, November 2012, Pages: 406–416, Jianbin Tong, Cao Huang, Fangfang Bi, Qinxue Wu, Bo Huang and Hongxia Zhou

    Version of Record online : 8 OCT 2012, DOI: 10.1111/jnc.12014

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    Stress granules in neurodegeneration – lessons learnt from TAR DNA binding protein of 43 kDa and fused in sarcoma

    The FEBS Journal

    Volume 280, Issue 18, September 2013, Pages: 4348–4370, Eva Bentmann, Christian Haass and Dorothee Dormann

    Version of Record online : 9 MAY 2013, DOI: 10.1111/febs.12287

  18. Hyperproduction of IL-6 caused by aberrant TDP-43 overexpression in high-fat diet-induced obese mice

    FEBS Letters

    Volume 589, Issue 15, July 08, 2015, Pages: 1825–1831, Sungwook Lee, Taeyun A. Lee, Su Jin Song, Taesun Park and Boyoun Park

    Version of Record online : 30 MAY 2015, DOI: 10.1016/j.febslet.2015.05.040

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    Significance and limitation of the pathological classification of TDP-43 proteinopathy

    Neuropathology

    Volume 34, Issue 6, December 2014, Pages: 578–588, Tetsuaki Arai

    Version of Record online : 8 SEP 2014, DOI: 10.1111/neup.12138

  20. Detection of TDP-43 oligomers in frontotemporal lobar degeneration–TDP

    Annals of Neurology

    Volume 78, Issue 2, August 2015, Pages: 211–221, Patricia F. Kao, Yun-Ru Chen, Xiao-Bo Liu, Charles DeCarli, William W. Seeley and Lee-Way Jin

    Version of Record online : 30 JUN 2015, DOI: 10.1002/ana.24431