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There are 8664 results for: content related to: Levels of DNAJB family members (HSP40) correlate with disease onset in patients with spinocerebellar ataxia type 3

  1. Cellular protein quality control and the evolution of aggregates in spinocerebellar ataxia type 3 (SCA3)

    Neuropathology and Applied Neurobiology

    Volume 38, Issue 6, October 2012, Pages: 548–558, K. Seidel, M. Meister, G. J. Dugbartey, M. P. Zijlstra, J. Vinet, E. R. P. Brunt, F. W. van Leeuwen, U. Rüb, H. H. Kampinga and W. F. A. den Dunnen

    Article first published online : 17 SEP 2012, DOI: 10.1111/j.1365-2990.2011.01220.x

  2. CDK5 protects from caspase-induced Ataxin-3 cleavage and neurodegeneration

    Journal of Neurochemistry

    Volume 129, Issue 6, June 2014, Pages: 1013–1023, Jan Liman, Sebastian Deeg, Aaron Voigt, Hannes Voßfeldt, Christoph P. Dohm, André Karch, Jochen Weishaupt, Jörg B. Schulz, Mathias Bähr and Pawel Kermer

    Article first published online : 24 MAR 2014, DOI: 10.1111/jnc.12684

  3. You have free access to this content
    Caspase-mediated proteolysis of the polyglutamine disease protein ataxin-3

    Journal of Neurochemistry

    Volume 89, Issue 4, May 2004, Pages: 908–918, Sarah J Shoesmith Berke, Francisca A Flores Schmied, Ewout R. Brunt, Lisa M. Ellerby and Henry L. Paulson

    Article first published online : 8 APR 2004, DOI: 10.1111/j.1471-4159.2004.02369.x

  4. You have free access to this content
    Gene expression profiling of porcine skeletal muscle in the early recovery phase following acute physical activity

    Experimental Physiology

    Volume 97, Issue 7, July 2012, Pages: 833–848, Jeanette H. Jensen, Lene N. Conley, Jakob Hedegaard, Mathilde Nielsen, Jette F. Young, Niels Oksbjerg, Henrik Hornshøj, Christian Bendixen and Bo Thomsen

    Article first published online : 31 MAY 2012, DOI: 10.1113/expphysiol.2011.063727

  5. Spinocerebellar Ataxia Type 3 (SCA3): Thalamic Neurodegeneration Occurs Independently from Thalamic Ataxin-3 Immunopositive Neuronal Intranuclear Inclusions

    Brain Pathology

    Volume 16, Issue 3, July 2006, Pages: 218–227, Udo Rüb, Rob A.I. De Vos, Ewout R. Brunt, Tamás Sebestény, Ludger Schöls, Georg Auburger, Jürgen Bohl, Estifanos Ghebremedhin, Kristin Gierga, Kay Seidel, Wilfred Den Dunnen, Helmut Heinsen, Henry Paulson and Thomas Deller

    Article first published online : 4 AUG 2006, DOI: 10.1111/j.1750-3639.2006.00022.x

  6. Schwann cell involvement in the peripheral neuropathy of spinocerebellar ataxia type 3

    Neuropathology and Applied Neurobiology

    Volume 40, Issue 5, August 2014, Pages: 628–639, Noriaki Suga, Masahisa Katsuno, Haruki Koike, Haruhiko Banno, Keisuke Suzuki, Atsushi Hashizume, Tomoo Mano, Masahiro Iijima, Yuichi Kawagashira, Masaaki Hirayama, Tomohiko Nakamura, Hirohisa Watanabe, Fumiaki Tanaka and Gen Sobue

    Article first published online : 1 JUL 2014, DOI: 10.1111/nan.12055

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    Structural and functional analysis of ataxin-2 and ataxin-3

    European Journal of Biochemistry

    Volume 271, Issue 15, August 2004, Pages: 3155–3170, Mario Albrecht, Michael Golatta, Ullrich Wüllner and Thomas Lengauer

    Article first published online : 15 JUL 2004, DOI: 10.1111/j.1432-1033.2004.04245.x

  8. Degeneration of ingestion-related brainstem nuclei in spinocerebellar ataxia type 2, 3, 6 and 7

    Neuropathology and Applied Neurobiology

    Volume 32, Issue 6, December 2006, Pages: 635–649, U. Rüb, E. R. Brunt, E. Petrasch-Parwez, L. Schöls, D. Theegarten, G. Auburger, K. Seidel, C. Schultz, K. Gierga, H. Paulson, C. Van Broeckhoven, T. Deller and R. A. I. De Vos

    Article first published online : 8 AUG 2006, DOI: 10.1111/j.1365-2990.2006.00772.x

  9. Inducible 70 kDa heat shock proteins protect embryos from teratogen-induced exencephaly: Analysis using Hspa1a/a1b knockout mice

    Birth Defects Research Part A: Clinical and Molecular Teratology

    Volume 85, Issue 8, August 2009, Pages: 732–740, Marianne Barrier, David J. Dix and Philip E. Mirkes

    Article first published online : 28 JUL 2009, DOI: 10.1002/bdra.20610

  10. An Isoform of Ataxin-3 Accumulates in the Nucleus of Neuronal Cells in Affected Brain Regions of SCA3 Patients

    Brain Pathology

    Volume 8, Issue 4, October 1998, Pages: 669–679, Thorsten Schmidt, G. Bernhard Landwehrmeyer, Ina Schmitt, Yvon Trottier, Georg Auburger, Franco Laccone, Thomas Klockgether, Michael Völpel, Jörg T. Epplen, Ludger Schöls and Olaf Riess

    Article first published online : 5 APR 2006, DOI: 10.1111/j.1750-3639.1998.tb00193.x

  11. Differential proteomic analysis of lymphatic, venous, and arterial endothelial cells extracted from bovine mesenteric vessels


    Volume 10, Issue 8, No. 8 April 2010, Pages: 1658–1672, Vicky P. K. H. Nguyen, George Hanna, Natalie Rodrigues, Katerina Pizzuto, Eric Yang, Paul Van Slyke, Harold Kim, Stephen H. Chen and Daniel J. Dumont

    Article first published online : 22 FEB 2010, DOI: 10.1002/pmic.200900594

  12. Structural modeling of ataxin-3 reveals distant homology to adaptins

    Proteins: Structure, Function, and Bioinformatics

    Volume 50, Issue 2, 1 February 2003, Pages: 355–370, Mario Albrecht, Daniel Hoffmann, Bernd O. Evert, Ina Schmitt, Ullrich Wüllner and Thomas Lengauer

    Article first published online : 12 DEC 2002, DOI: 10.1002/prot.10280

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    Poster Presentations

    Movement Disorders

    Volume 27, Issue S1, June 2012, Pages: S1–S523,

    Article first published online : 19 JUN 2012, DOI: 10.1002/mds.25051

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    Molecular clearance of ataxin-3 is regulated by a mammalian E4

    The EMBO Journal

    Volume 23, Issue 3, February 11, 2004, Pages: 659–669, Masaki Matsumoto, Masayoshi Yada, Shigetsugu Hatakeyama, Hiroshi Ishimoto, Teiichi Tanimura, Shoji Tsuji, Akira Kakizuka, Masatoshi Kitagawa and Keiichi I Nakayama

    Article first published online : 29 JAN 2004, DOI: 10.1038/sj.emboj.7600081

  15. Insights into function and regulation of small heat shock protein 25 (HSPB1) in a mouse model with targeted gene disruption


    Volume 45, Issue 8, August 2007, Pages: 487–501, Lei Huang, Jin-Na Min, Shane Masters, Nahid F. Mivechi and Demetrius Moskophidis

    Article first published online : 27 JUL 2007, DOI: 10.1002/dvg.20319

  16. Regulation of apoptosis by heat shock proteins

    IUBMB Life

    Volume 66, Issue 5, May 2014, Pages: 327–338, Donna Kennedy, Richard Jäger, Dick D Mosser and Afshin Samali

    Article first published online : 26 MAY 2014, DOI: 10.1002/iub.1274

  17. Microarray analysis of cellular thermotolerance

    Lasers in Surgery and Medicine

    Volume 42, Issue 10, December 2010, Pages: 912–925, Josh T. Beckham, Gerald J. Wilmink, Susan R. Opalenik, Mark A. Mackanos, Alex A. Abraham, Keiko Takahashi, Chris H. Contag, Takamune Takahashi and E. Duco Jansen

    Article first published online : 18 JAN 2011, DOI: 10.1002/lsm.20983

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    The pathogenic mechanisms of polyglutamine diseases and current therapeutic strategies

    Journal of Neurochemistry

    Volume 110, Issue 6, September 2009, Pages: 1737–1765, Peter O. Bauer and Nobuyuki Nukina

    Article first published online : 23 JUL 2009, DOI: 10.1111/j.1471-4159.2009.06302.x

  19. HSPA1A is an important regulator of the stability and function of ZNF198 and its oncogenic derivative, ZNF198–FGFR1

    Journal of Cellular Biochemistry

    Volume 102, Issue 5, 1 December 2007, Pages: 1308–1317, Chitta S. Kasyapa, Padmaja Kunapuli and John K. Cowell

    Article first published online : 30 APR 2007, DOI: 10.1002/jcb.21362

  20. Degeneration of the central vestibular system in spinocerebellar ataxia type 3 (SCA3) patients and its possible clinical significance

    Neuropathology and Applied Neurobiology

    Volume 30, Issue 4, August 2004, Pages: 402–414, U. Rüb, E. R. Brunt, R. A. I. De Vos, D. Del Turco, K. Del Tredici, K. Gierga, C. Schultz, E. Ghebremedhin, K. Bürk, G. Auburger and H. Braak

    Article first published online : 4 MAY 2004, DOI: 10.1111/j.1365-2990.2004.00554.x