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There are 5669 results for: content related to: Levels of DNAJB family members (HSP40) correlate with disease onset in patients with spinocerebellar ataxia type 3

  1. Cellular protein quality control and the evolution of aggregates in spinocerebellar ataxia type 3 (SCA3)

    Neuropathology and Applied Neurobiology

    Volume 38, Issue 6, October 2012, Pages: 548–558, K. Seidel, M. Meister, G. J. Dugbartey, M. P. Zijlstra, J. Vinet, E. R. P. Brunt, F. W. van Leeuwen, U. Rüb, H. H. Kampinga and W. F. A. den Dunnen

    Article first published online : 17 SEP 2012, DOI: 10.1111/j.1365-2990.2011.01220.x

  2. Spinocerebellar Ataxia Type 3 (SCA3): Thalamic Neurodegeneration Occurs Independently from Thalamic Ataxin-3 Immunopositive Neuronal Intranuclear Inclusions

    Brain Pathology

    Volume 16, Issue 3, July 2006, Pages: 218–227, Udo Rüb, Rob A.I. De Vos, Ewout R. Brunt, Tamás Sebestény, Ludger Schöls, Georg Auburger, Jürgen Bohl, Estifanos Ghebremedhin, Kristin Gierga, Kay Seidel, Wilfred Den Dunnen, Helmut Heinsen, Henry Paulson and Thomas Deller

    Article first published online : 4 AUG 2006, DOI: 10.1111/j.1750-3639.2006.00022.x

  3. CDK5 protects from caspase-induced Ataxin-3 cleavage and neurodegeneration

    Journal of Neurochemistry

    Volume 129, Issue 6, June 2014, Pages: 1013–1023, Jan Liman, Sebastian Deeg, Aaron Voigt, Hannes Voßfeldt, Christoph P. Dohm, André Karch, Jochen Weishaupt, Jörg B. Schulz, Mathias Bähr and Pawel Kermer

    Article first published online : 24 MAR 2014, DOI: 10.1111/jnc.12684

  4. Degeneration of ingestion-related brainstem nuclei in spinocerebellar ataxia type 2, 3, 6 and 7

    Neuropathology and Applied Neurobiology

    Volume 32, Issue 6, December 2006, Pages: 635–649, U. Rüb, E. R. Brunt, E. Petrasch-Parwez, L. Schöls, D. Theegarten, G. Auburger, K. Seidel, C. Schultz, K. Gierga, H. Paulson, C. Van Broeckhoven, T. Deller and R. A. I. De Vos

    Article first published online : 8 AUG 2006, DOI: 10.1111/j.1365-2990.2006.00772.x

  5. You have free access to this content
    Caspase-mediated proteolysis of the polyglutamine disease protein ataxin-3

    Journal of Neurochemistry

    Volume 89, Issue 4, May 2004, Pages: 908–918, Sarah J Shoesmith Berke, Francisca A Flores Schmied, Ewout R. Brunt, Lisa M. Ellerby and Henry L. Paulson

    Article first published online : 8 APR 2004, DOI: 10.1111/j.1471-4159.2004.02369.x

  6. Schwann cell involvement in the peripheral neuropathy of spinocerebellar ataxia type 3

    Neuropathology and Applied Neurobiology

    Volume 40, Issue 5, August 2014, Pages: 628–639, Noriaki Suga, Masahisa Katsuno, Haruki Koike, Haruhiko Banno, Keisuke Suzuki, Atsushi Hashizume, Tomoo Mano, Masahiro Iijima, Yuichi Kawagashira, Masaaki Hirayama, Tomohiko Nakamura, Hirohisa Watanabe, Fumiaki Tanaka and Gen Sobue

    Article first published online : 1 JUL 2014, DOI: 10.1111/nan.12055

  7. You have free access to this content
    Poster Presentations

    Movement Disorders

    Volume 27, Issue S1, June 2012, Pages: S1–S523,

    Article first published online : 19 JUN 2012, DOI: 10.1002/mds.25051

  8. Structural modeling of ataxin-3 reveals distant homology to adaptins

    Proteins: Structure, Function, and Bioinformatics

    Volume 50, Issue 2, 1 February 2003, Pages: 355–370, Mario Albrecht, Daniel Hoffmann, Bernd O. Evert, Ina Schmitt, Ullrich Wüllner and Thomas Lengauer

    Article first published online : 12 DEC 2002, DOI: 10.1002/prot.10280

  9. You have free access to this content
    Structural and functional analysis of ataxin-2 and ataxin-3

    European Journal of Biochemistry

    Volume 271, Issue 15, August 2004, Pages: 3155–3170, Mario Albrecht, Michael Golatta, Ullrich Wüllner and Thomas Lengauer

    Article first published online : 15 JUL 2004, DOI: 10.1111/j.1432-1033.2004.04245.x

  10. Degeneration of the central vestibular system in spinocerebellar ataxia type 3 (SCA3) patients and its possible clinical significance

    Neuropathology and Applied Neurobiology

    Volume 30, Issue 4, August 2004, Pages: 402–414, U. Rüb, E. R. Brunt, R. A. I. De Vos, D. Del Turco, K. Del Tredici, K. Gierga, C. Schultz, E. Ghebremedhin, K. Bürk, G. Auburger and H. Braak

    Article first published online : 4 MAY 2004, DOI: 10.1111/j.1365-2990.2004.00554.x

  11. Protein surveillance machinery in brains with spinocerebellar ataxia type 3: Redistribution and differential recruitment of 26S proteasome subunits and chaperones to neuronal intranuclear inclusions

    Annals of Neurology

    Volume 51, Issue 3, March 2002, Pages: 302–310, Thorsten Schmidt, Katrin S. Lindenberg, Antje Krebs, Ludger Schöls, Franco Laccone, Jochen Herms, Martin Rechsteiner, Olaf Riess and G. Bernhard Landwehrmeyer

    Article first published online : 27 FEB 2002, DOI: 10.1002/ana.10101

  12. You have free access to this content
    The pathogenic mechanisms of polyglutamine diseases and current therapeutic strategies

    Journal of Neurochemistry

    Volume 110, Issue 6, September 2009, Pages: 1737–1765, Peter O. Bauer and Nobuyuki Nukina

    Article first published online : 23 JUL 2009, DOI: 10.1111/j.1471-4159.2009.06302.x

  13. You have free access to this content
    Molecular clearance of ataxin-3 is regulated by a mammalian E4

    The EMBO Journal

    Volume 23, Issue 3, February 11, 2004, Pages: 659–669, Masaki Matsumoto, Masayoshi Yada, Shigetsugu Hatakeyama, Hiroshi Ishimoto, Teiichi Tanimura, Shoji Tsuji, Akira Kakizuka, Masatoshi Kitagawa and Keiichi I Nakayama

    Article first published online : 29 JAN 2004, DOI: 10.1038/sj.emboj.7600081

  14. Involvement of the auditory brainstem system in spinocerebellar ataxia type 2 (SCA2), type 3 (SCA3) and type 7 (SCA7)

    Neuropathology and Applied Neurobiology

    Volume 34, Issue 5, October 2008, Pages: 479–491, F. Hoche, K. Seidel, E. R. Brunt, G. Auburger, L. Schöls, K. Bürk, R. A. De Vos, W. Den Dunnen, I. Bechmann, R. Egensperger, C. Van Broeckhoven, K. Gierga, T. Deller and U. Rüb

    Article first published online : 24 JAN 2008, DOI: 10.1111/j.1365-2990.2007.00933.x

  15. The HSPB8-BAG3 chaperone complex is upregulated in astrocytes in the human brain affected by protein aggregation diseases

    Neuropathology and Applied Neurobiology

    Volume 38, Issue 1, February 2012, Pages: 39–53, K. Seidel, J. Vinet, W. F. A. den Dunnen, E. R. Brunt, M. Meister, A. Boncoraglio, M. P. Zijlstra, H. W. G. M. Boddeke, U. Rüb, H. H. Kampinga and S. Carra

    Article first published online : 6 JAN 2012, DOI: 10.1111/j.1365-2990.2011.01198.x

  16. Decreased antioxidant enzyme activity and increased mitochondrial DNA damage in cellular models of Machado-Joseph disease

    Journal of Neuroscience Research

    Volume 87, Issue 8, June 2009, Pages: 1884–1891, Ya-Chun Yu, Chen-Ling Kuo, Wen-Ling Cheng, Chin-San Liu and Mingli Hsieh

    Article first published online : 30 JAN 2009, DOI: 10.1002/jnr.22011

  17. Abnormal RNA structures (RNA foci) containing a penta-nucleotide repeat (UGGAA)n in the Purkinje cell nucleus is associated with spinocerebellar ataxia type 31 pathogenesis

    Neuropathology

    Volume 33, Issue 6, December 2013, Pages: 600–611, Yusuke Niimi, Makoto Takahashi, Emiko Sugawara, Shigeaki Umeda, Masato Obayashi, Nozomu Sato, Taro Ishiguro, Miwa Higashi, Yoshinobu Eishi, Hidehiro Mizusawa and Kinya Ishikawa

    Article first published online : 22 APR 2013, DOI: 10.1111/neup.12032

  18. You have free access to this content
    Poster Presentations

    Movement Disorders

    Volume 29, Issue S1, May 2014, Pages: S1–S571,

    Article first published online : 6 JUN 2014, DOI: 10.1002/mds.25914

  19. Absence of spinocerebellar ataxia type 3/Machado–Joseph disease within ataxic patients in the Czech population

    European Journal of Neurology

    Volume 12, Issue 11, November 2005, Pages: 851–857, P. O. Bauer, A. Zumrova, V. Matoska, T. Marikova, S. Krilova, A. Boday, B. Singh and P. Goetz

    Article first published online : 20 OCT 2005, DOI: 10.1111/j.1468-1331.2005.01090.x

  20. Regulation of apoptosis by heat shock proteins

    IUBMB Life

    Volume 66, Issue 5, May 2014, Pages: 327–338, Donna Kennedy, Richard Jäger, Dick D Mosser and Afshin Samali

    Article first published online : 26 MAY 2014, DOI: 10.1002/iub.1274