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There are 14095 results for: content related to: Intermittent-relapsing pyruvate dehydrogenase complex deficiency: a case with clinical, biochemical, and neuroradiological reversibility

  1. Studies on the Bovine Brain Pyruvate Dehydrogenase Complex Using the Antibodies Against Kidney Enzyme Complex

    Journal of Neurochemistry

    Volume 43, Issue 5, November 1984, Pages: 1352–1358, Kwan-Fu Rex Sheu and Young Tai Kim

    Article first published online : 5 OCT 2006, DOI: 10.1111/j.1471-4159.1984.tb05394.x

  2. Immunochemical Characterization of Pyruvate Dehydrogenase Complex in Rat Brain

    Journal of Neurochemistry

    Volume 44, Issue 2, February 1985, Pages: 593–599, Kwan-Fu Rex Sheu, James C. K. Lai, Young Tai Kim, Gary Dorante and Jennifer Bagg

    Article first published online : 5 OCT 2006, DOI: 10.1111/j.1471-4159.1985.tb05453.x

  3. Relationship Between Activation State of Pyruvate Dehydrogenase Complex and Rate of Pyruvate Oxidation in Isolated Cerebro-Cortical Mitochondria: Effects of Potassium Ions and Adenine Nucleotides

    Journal of Neurochemistry

    Volume 45, Issue 6, December 1985, Pages: 1861–1868, James C. K. Lai and Kwan-Fu Rex Sheu

    Article first published online : 5 OCT 2006, DOI: 10.1111/j.1471-4159.1985.tb10544.x

  4. Pyruvate Dehydrogenase Phosphate (PDHb) Phosphatase in Brain: Activity, Properties, and Subcellular Localization

    Journal of Neurochemistry

    Volume 40, Issue 5, May 1983, Pages: 1366–1372, Kwan-Fu Rex Sheu, James C. K. Lai and John P. Blass

    Article first published online : 28 JUN 2008, DOI: 10.1111/j.1471-4159.1983.tb13578.x

  5. An immunochemical study of the pyruvate dehydrogenase deficit in Alzheimer's disease brain

    Annals of Neurology

    Volume 17, Issue 5, May 1985, Pages: 444–449, Dr Kwan-Fu Rex Sheu, Young-Tai Kim, John P. Blass and Marc E Weksler

    Article first published online : 7 OCT 2004, DOI: 10.1002/ana.410170505

  6. Mutational study in the PDHA1 gene of 40 patients suspected of pyruvate dehydrogenase complex deficiency

    Clinical Genetics

    Volume 77, Issue 5, May 2010, Pages: 474–482, E Quintana, L Gort, C Busquets, A Navarro-Sastre, W Lissens, S Moliner, M Lluch, MA Vilaseca, L De Meirleir, A Ribes, P Briones and PDH Working Group

    Article first published online : 10 DEC 2009, DOI: 10.1111/j.1399-0004.2009.01313.x

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    Erratum

    Vol. 78, Issue 1, 101, Article first published online: 7 JUN 2010

  7. Studies on the Pyruvate Dehydrogenase Complex in Brain with the Arylamine Acetyltransferase-Coupled Assay

    Journal of Neurochemistry

    Volume 38, Issue 6, June 1982, Pages: 1627–1636, Hanna Ksiezak-Reding, John P. Blass and Gary E. Gibson

    Article first published online : 5 OCT 2006, DOI: 10.1111/j.1471-4159.1982.tb06643.x

  8. Properties and Regional Distribution of Pyruvate Dehydrogenase Kinase in Rat Brain

    Journal of Neurochemistry

    Volume 42, Issue 1, January 1984, Pages: 230–236, Kwan-Fu Rex Sheu, James C. K. Lai and John P. Blass

    Article first published online : 5 OCT 2006, DOI: 10.1111/j.1471-4159.1984.tb09722.x

  9. The Pyruvate Dehydrogenase Complex: Cloning of the Rat Somatic El α Subunit and Its Coordinate Expression with the mRNAs for the E1β E2, and E3 Catalytic Subunits in Developing Rat Brain

    Journal of Neurochemistry

    Volume 62, Issue 5, May 1994, Pages: 1682–1690, Tim E. Cullingford, John B. Clark and Ian R. Phillips

    Article first published online : 28 JUN 2008, DOI: 10.1046/j.1471-4159.1994.62051682.x

  10. You have full text access to this OnlineOpen article
    The Pyruvate Dehydrogenase Complex Is Partially Inactivated During Early Recirculation Following Short-Term Forebrain Ischemia in Rats

    Journal of Neurochemistry

    Volume 70, Issue 1, January 1998, Pages: 233–241, Emad Zaidan, Kwan-Fu Rex Sheu and Neil R. Sims

    Article first published online : 14 NOV 2002, DOI: 10.1046/j.1471-4159.1998.70010233.x

  11. Pyruvate Dehydrogenase Activity in Osmotically Shocked Rat Brain Mitochondria: Stimulation by Oxaloacetate

    Journal of Neurochemistry

    Volume 50, Issue 3, March 1988, Pages: 673–680, Richard H. Haas, Geoffrey Thompson, Bernard Morris, Kelly Conright and Torre Andrews

    Article first published online : 5 OCT 2006, DOI: 10.1111/j.1471-4159.1988.tb02966.x

  12. Decreased pyruvate dehydrogenase complex activity in Huntington and Alzheimer brain

    Annals of Neurology

    Volume 13, Issue 1, January 1983, Pages: 72–78, Dr Sandro Sorbi, Edward D. Bird and John P. Blass

    Article first published online : 7 OCT 2004, DOI: 10.1002/ana.410130116

  13. You have free access to this content
    Autoantibodies to mitochondrial and centromere antigens in primary biliary cirrhosis and systemic sclerosis

    Clinical & Experimental Immunology

    Volume 81, Issue 2, August 1990, Pages: 244–249, N. J. McHUGH, I. E. JAMES, K. FAIRBURN and P. J. MADDISON

    Article first published online : 28 JUN 2008, DOI: 10.1111/j.1365-2249.1990.tb03325.x

  14. Effects of Dichloroacetate on Brain Tissue Pyruvate Dehydrogenase

    Journal of Neurochemistry

    Volume 41, Issue 4, April 1983, Pages: 1052–1056, Owen B. Evans

    Article first published online : 5 OCT 2006, DOI: 10.1111/j.1471-4159.1983.tb09050.x

  15. You have full text access to this OnlineOpen article
    Kinetics and specificity of reductive acylation of wild-type and mutated lipoyl domains of 2-oxo-acid dehydrogenase complexes from Azotobacter vinelandii

    European Journal of Biochemistry

    Volume 252, Issue 1, February (II) 1998, Pages: 45–50, Axel Berg, Adrie H. Westphal, Hans J. Bosma and Aart De Kok

    Article first published online : 25 DEC 2001, DOI: 10.1046/j.1432-1327.1998.2520045.x

  16. You have full text access to this OnlineOpen article
    Sequential 1H and 15N Nuclear Magnetic Resonance Assignments and Secondary Structure of the Lipoyl Domain of the 2-Oxoglutarate Dehydrogenase Complex from Azotobacter Vinelandii

    European Journal of Biochemistry

    Volume 234, Issue 1, November 1995, Pages: 148–159, Axel Berg, Otto Smits, Arie de Kok and Jacques Vervoort

    Article first published online : 7 SEP 2004, DOI: 10.1111/j.1432-1033.1995.148_c.x

  17. Pyruvate Dehydrogenase Activity in Regions of the Rat Brain During Postnatal Development

    Journal of Neurochemistry

    Volume 43, Issue 1, July 1984, Pages: 280–282, Roger F. Butterworth and Jean-François Giguère

    Article first published online : 5 OCT 2006, DOI: 10.1111/j.1471-4159.1984.tb06710.x

  18. A case of pyruvate dehydrogenase E1α subunit deficiency with antenatal brain dysgenesis demonstrated by prenatal sonography and magnetic resonance imaging

    Journal of Clinical Ultrasound

    Volume 40, Issue 4, May 2012, Pages: 234–238, Shunsuke Tamaru, Akihiko Kikuchi, Kimiyo Takagi, Jiu Okuno, Kaori Ishikawa, Shinya Imada, Tsuguhiro Horikoshi, Yu-ichi Goto and Shinichi Hirabayashi

    Article first published online : 2 AUG 2011, DOI: 10.1002/jcu.20864

  19. Novel mutation (R263X) of the E1α subunit in pyruvate dehydrogenase complex deficiency

    Pediatrics International

    Volume 52, Issue 4, August 2010, Pages: e181–e183, Satoshi Sato, Hiroaki Ioi, Yasuyo Kashiwagi, Hisashi Kawashima, Tasuku Miyajima, Etsuo Naito and Akinori Hoshika

    Article first published online : 17 AUG 2010, DOI: 10.1111/j.1442-200X.2010.03112.x

  20. Differences in sensitivity to NADH of purified pyruvate dehydrogenase complexes of Enterococcus faecalis, Lactococcus lactis, Azotobacter vinelandii and Escherichia coli: Implications for their activity in vivo

    FEMS Microbiology Letters

    Volume 114, Issue 3, December 1993, Pages: 279–283, Jacky L. Snoep, Mark R. de Graef, Adrie H. Westphal, Arie de Kok, M. Joost Teixeira de Mattos and Oense M. Neijssel

    Article first published online : 17 JAN 2006, DOI: 10.1111/j.1574-6968.1993.tb06586.x