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There are 7563 results for: content related to: A novel variant of human superoxide dismutase 1 harboring amyotrophic lateral sclerosis-associated and experimental mutations in metal-binding residues and free cysteines lacks toxicity in vivo

  1. You have full text access to this OnlineOpen article
    SOD1 silencing in motoneurons or glia rescues neuromuscular function in ALS mice

    Annals of Clinical and Translational Neurology

    Volume 2, Issue 2, February 2015, Pages: 167–184, Elisabeth Dirren, Julianne Aebischer, Cylia Rochat, Christopher Towne, Bernard L. Schneider and Patrick Aebischer

    Version of Record online : 15 JAN 2015, DOI: 10.1002/acn3.162

  2. You have full text access to this OnlineOpen article
    Senescence marker protein-30/superoxide dismutase 1 double knockout mice exhibit increased oxidative stress and hepatic steatosis

    FEBS Open Bio

    Volume 4, Issue 1, January 01, 2014, Pages: 522–532, Yoshitaka Kondo, Hirofumi Masutomi, Yoshihiro Noda, Yusuke Ozawa, Keita Takahashi, Setsuko Handa, Naoki Maruyama, Takahiko Shimizu and Akihito Ishigami

    Version of Record online : 24 MAY 2014, DOI: 10.1016/j.fob.2014.05.003

  3. Extracellular aggregated Cu/Zn superoxide dismutase activates microglia to give a cytotoxic phenotype

    Glia

    Volume 61, Issue 3, March 2013, Pages: 409–419, Kate Roberts, Rafaa Zeineddine, Lisa Corcoran, Wen Li, Iain L. Campbell and Justin J. Yerbury

    Version of Record online : 22 DEC 2012, DOI: 10.1002/glia.22444

  4. A revisited folding reporter for quantitative assay of protein misfolding and aggregation in mammalian cells

    Biotechnology Journal

    Volume 7, Issue 10, October 2012, Pages: 1297–1307, Simpson Gregoire and Dr. Inchan Kwon

    Version of Record online : 27 JUN 2012, DOI: 10.1002/biot.201200103

  5. You have free access to this content
    An examination of αB-crystallin as a modifier of SOD1 aggregate pathology and toxicity in models of familial amyotrophic lateral sclerosis

    Journal of Neurochemistry

    Volume 113, Issue 5, June 2010, Pages: 1092–1100, Celeste M. Karch and David R. Borchelt

    Version of Record online : 7 JAN 2010, DOI: 10.1111/j.1471-4159.2010.06572.x

  6. Targeting miR-155 restores abnormal microglia and attenuates disease in SOD1 mice

    Annals of Neurology

    Volume 77, Issue 1, January 2015, Pages: 75–99, Oleg Butovsky, Mark P. Jedrychowski, Ron Cialic, Susanne Krasemann, Gopal Murugaiyan, Zain Fanek, David J. Greco, Pauline M. Wu, Camille E. Doykan, Olga Kiner, Robert J. Lawson, Matthew P. Frosch, Nathalie Pochet, Rachid El Fatimy, Anna M. Krichevsky, Steven P. Gygi, Hans Lassmann, James Berry, Merit E. Cudkowicz and Howard L. Weiner

    Version of Record online : 27 NOV 2014, DOI: 10.1002/ana.24304

    Corrected by:

    Corrigendum: Corrigendum: Targeting miR-155 restores abnormal microglia and attenuates disease in SOD1 mice

    Vol. 77, Issue 6, 1085, Version of Record online: 22 APR 2015

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    Cytoplasmic superoxide causes bone fragility owing to low-turnover osteoporosis and impaired collagen cross-linking

    Journal of Bone and Mineral Research

    Volume 26, Issue 11, November 2011, Pages: 2682–2694, Hidetoshi Nojiri, Yoshitomo Saita, Daichi Morikawa, Keiji Kobayashi, Chizuru Tsuda, Tsuyoshi Miyazaki, Mitsuru Saito, Keishi Marumo, Ikuho Yonezawa, Kazuo Kaneko, Takuji Shirasawa and Takahiko Shimizu

    Version of Record online : 20 OCT 2011, DOI: 10.1002/jbmr.489

  8. You have free access to this content
    Intracerebroventricular infusion of monoclonal antibody or its derived Fab fragment against misfolded forms of SOD1 mutant delays mortality in a mouse model of ALS

    Journal of Neurochemistry

    Volume 113, Issue 5, June 2010, Pages: 1188–1199, Francois Gros-Louis, Geneviève Soucy, Roxanne Larivière and Jean-Pierre Julien

    Version of Record online : 14 MAR 2010, DOI: 10.1111/j.1471-4159.2010.06683.x

  9. You have free access to this content
    Characterization of Cu,Zn superoxide dismutase (SOD1) gene knock-out mutant of Cryptococcus neoformans var. gattii: role in biology and virulence

    Molecular Microbiology

    Volume 47, Issue 6, March 2003, Pages: 1681–1694, Srinivas D. Narasipura, Jeffrey G. Ault, Melissa J. Behr, Vishnu Chaturvedi and Sudha Chaturvedi

    Version of Record online : 5 MAR 2003, DOI: 10.1046/j.1365-2958.2003.03393.x

  10. ALS and the Copper Chaperone CCS

    Protein Chaperones and Protection from Neurodegenerative Diseases

    Marjatta Son, Jeffrey L. Elliott, Pages: 315–357, 2011

    Published Online : 6 JUN 2011, DOI: 10.1002/9781118063903.ch10

  11. You have full text access to this Open Access content
    Nutrient-dependent requirement for SOD1 in lifespan extension by protein restriction in Drosophila melanogaster

    Aging Cell

    Volume 11, Issue 5, October 2012, Pages: 783–793, Xiaoping Sun, Toshimitsu Komatsu, Jinhwan Lim, Mara Laslo, Jason Yolitz, Cecilia Wang, Luc Poirier, Thomas Alberico and Sige Zou

    Version of Record online : 3 JUL 2012, DOI: 10.1111/j.1474-9726.2012.00842.x

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    Mapping superoxide dismutase 1 domains of non-native interaction: roles of intra- and intermolecular disulfide bonding in aggregation

    Journal of Neurochemistry

    Volume 96, Issue 5, March 2006, Pages: 1277–1288, Jiou Wang, Guilian Xu and David R. Borchelt

    Version of Record online : 25 JAN 2006, DOI: 10.1111/j.1471-4159.2005.03642.x

  13. Familial amyotrophic lateral sclerosis

    Muscle & Nerve

    Volume 25, Issue 2, February 2002, Pages: 135–159, Collette K. Hand and Guy A. Rouleau

    Version of Record online : 11 FEB 2002, DOI: 10.1002/mus.10001

  14. You have full text access to this OnlineOpen article
    Role of superoxide–nitric oxide interactions in the accelerated age-related loss of muscle mass in mice lacking Cu,Zn superoxide dismutase

    Aging Cell

    Volume 10, Issue 5, October 2011, Pages: 749–760, Giorgos K. Sakellariou, Deborah Pye, Aphrodite Vasilaki, Lea Zibrik, Jesus Palomero, Tabitha Kabayo, Francis McArdle, Holly Van Remmen, Arlan Richardson, James G. Tidball, Anne McArdle and Malcolm J. Jackson

    Version of Record online : 6 MAY 2011, DOI: 10.1111/j.1474-9726.2011.00709.x

  15. You have full text access to this Open Access content
    Dietary restriction attenuates age-associated muscle atrophy by lowering oxidative stress in mice even in complete absence of CuZnSOD

    Aging Cell

    Volume 11, Issue 5, October 2012, Pages: 770–782, Young C. Jang, Yuhong Liu, Christopher R. Hayworth, Arunabh Bhattacharya, Michael S. Lustgarten, Florian L. Muller, Asish Chaudhuri, Wenbo Qi, Yan Li, Jing-Yi Huang, Eric Verdin, Arlan Richardson and Holly Van Remmen

    Version of Record online : 2 AUG 2012, DOI: 10.1111/j.1474-9726.2012.00843.x

  16. You have free access to this content
    S-nitrosylated protein disulfide isomerase contributes to mutant SOD1 aggregates in amyotrophic lateral sclerosis

    Journal of Neurochemistry

    Volume 124, Issue 1, January 2013, Pages: 45–58, Xueping Chen, Xiaosha Zhang, Chen Li, Teng Guan, Huifang Shang, Liying Cui, Xin-Min Li and Jiming Kong

    Version of Record online : 1 NOV 2012, DOI: 10.1111/jnc.12046

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    Substantially elevating the levels of αB-crystallin in spinal motor neurons of mutant SOD1 mice does not significantly delay paralysis or attenuate mutant protein aggregation

    Journal of Neurochemistry

    Volume 133, Issue 3, May 2015, Pages: 452–464, Guilian Xu, Susan Fromholt, Jacob I. Ayers, Hilda Brown, Zoe Siemienski, Keith W. Crosby, Christopher A. Mayer, Christopher Janus and David R. Borchelt

    Version of Record online : 26 JAN 2015, DOI: 10.1111/jnc.13022

  18. You have free access to this content
    Altered postnatal maturation of electrical properties in spinal motoneurons in a mouse model of amyotrophic lateral sclerosis

    The Journal of Physiology

    Volume 589, Issue 9, May 2011, Pages: 2245–2260, K. A. Quinlan, J. E. Schuster, R. Fu, T. Siddique and C. J. Heckman

    Version of Record online : 27 APR 2011, DOI: 10.1113/jphysiol.2010.200659

  19. Excitability properties of mouse motor axons in the mutant SOD1G93A model of amyotrophic lateral sclerosis

    Muscle & Nerve

    Volume 41, Issue 6, June 2010, Pages: 774–784, Delphine Boërio, Bernadett Kalmar, Linda Greensmith and Hugh Bostock

    Version of Record online : 21 JAN 2010, DOI: 10.1002/mus.21579

  20. A novel monoclonal antibody reveals a conformational alteration shared by amyotrophic lateral sclerosis-linked SOD1 mutants

    Annals of Neurology

    Volume 72, Issue 5, November 2012, Pages: 739–749, Takao Fujisawa, Kengo Homma, Namiko Yamaguchi, Hisae Kadowaki, Naomi Tsuburaya, Isao Naguro, Atsushi Matsuzawa, Kohsuke Takeda, Yuji Takahashi, Jun Goto, Shoji Tsuji, Hideki Nishitoh and Hidenori Ichijo

    Version of Record online : 21 AUG 2012, DOI: 10.1002/ana.23668