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There are 11955 results for: content related to: Distinctive features of the D101N and D101G variants of superoxide dismutase 1; two mutations that produce rapidly progressing motor neuron disease

  1. You have free access to this content
    Mutant SOD1 inhibits ER-Golgi transport in amyotrophic lateral sclerosis

    Journal of Neurochemistry

    Volume 129, Issue 1, April 2014, Pages: 190–204, Julie D. Atkin, Manal A. Farg, Kai Ying Soo, Adam K. Walker, Mark Halloran, Bradley J. Turner, Phillip Nagley and Malcolm K. Horne

    Version of Record online : 13 NOV 2013, DOI: 10.1111/jnc.12493

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    S-nitrosylated protein disulfide isomerase contributes to mutant SOD1 aggregates in amyotrophic lateral sclerosis

    Journal of Neurochemistry

    Volume 124, Issue 1, January 2013, Pages: 45–58, Xueping Chen, Xiaosha Zhang, Chen Li, Teng Guan, Huifang Shang, Liying Cui, Xin-Min Li and Jiming Kong

    Version of Record online : 1 NOV 2012, DOI: 10.1111/jnc.12046

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    Transglutaminase 2 accelerates neuroinflammation in amyotrophic lateral sclerosis through interaction with misfolded superoxide dismutase 1

    Journal of Neurochemistry

    Volume 128, Issue 3, February 2014, Pages: 403–418, Miki Oono, Ayako Okado-Matsumoto, Akemi Shodai, Akemi Ido, Yasuyuki Ohta, Koji Abe, Takashi Ayaki, Hidefumi Ito, Ryosuke Takahashi, Naoyuki Taniguchi and Makoto Urushitani

    Version of Record online : 30 SEP 2013, DOI: 10.1111/jnc.12441

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    Mia40 and MINOS act in parallel with Ccs1 in the biogenesis of mitochondrial Sod1

    The FEBS Journal

    Volume 280, Issue 20, October 2013, Pages: 4943–4959, Aksana Varabyova, Ulrike Topf, Paulina Kwiatkowska, Lidia Wrobel, Magdalena Kaus-Drobek and Agnieszka Chacinska

    Version of Record online : 22 JUL 2013, DOI: 10.1111/febs.12409

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    Biochemical properties and in vivo effects of the SOD1 zinc-binding site mutant (H80G)

    Journal of Neurochemistry

    Volume 118, Issue 5, September 2011, Pages: 891–901, Marjatta Son, Uma Srikanth, Krishna Puttaparthi, Christina Luther and Jeffrey L. Elliott

    Version of Record online : 21 JUL 2011, DOI: 10.1111/j.1471-4159.2011.07360.x

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    Impaired post-translational folding of familial ALS-linked Cu, Zn superoxide dismutase mutants

    The EMBO Journal

    Volume 26, Issue 3, February 7, 2007, Pages: 855–866, Cami K Bruns and Ron R Kopito

    Version of Record online : 25 JAN 2007, DOI: 10.1038/sj.emboj.7601528

  7. You have full text access to this OnlineOpen article
    SOD1 silencing in motoneurons or glia rescues neuromuscular function in ALS mice

    Annals of Clinical and Translational Neurology

    Volume 2, Issue 2, February 2015, Pages: 167–184, Elisabeth Dirren, Julianne Aebischer, Cylia Rochat, Christopher Towne, Bernard L. Schneider and Patrick Aebischer

    Version of Record online : 15 JAN 2015, DOI: 10.1002/acn3.162

  8. Cis-suppression to arrest protein aggregation in mammalian cells

    Biotechnology and Bioengineering

    Volume 111, Issue 3, March 2014, Pages: 462–474, Simpson Gregoire, Shaojie Zhang, Joseph Costanzo, Kelly Wilson, Erik J. Fernandez and Inchan Kwon

    Version of Record online : 18 OCT 2013, DOI: 10.1002/bit.25119

  9. Lack of TNF-alpha receptor type 2 protects motor neurons in a cellular model of amyotrophic lateral sclerosis and in mutant SOD1 mice but does not affect disease progression

    Journal of Neurochemistry

    Volume 135, Issue 1, October 2015, Pages: 109–124, Massimo Tortarolo, Antonio Vallarola, Dario Lidonnici, Elisa Battaglia, Francesco Gensano, Gabriella Spaltro, Fabio Fiordaliso, Alessandro Corbelli, Stefano Garetto, Elisa Martini, Laura Pasetto, Marinos Kallikourdis, Valentina Bonetto and Caterina Bendotti

    Version of Record online : 4 JUN 2015, DOI: 10.1111/jnc.13154

  10. You have full text access to this OnlineOpen article
    Senescence marker protein-30/superoxide dismutase 1 double knockout mice exhibit increased oxidative stress and hepatic steatosis

    FEBS Open Bio

    Volume 4, Issue 1, January 01, 2014, Pages: 522–532, Yoshitaka Kondo, Hirofumi Masutomi, Yoshihiro Noda, Yusuke Ozawa, Keita Takahashi, Setsuko Handa, Naoki Maruyama, Takahiko Shimizu and Akihito Ishigami

    Version of Record online : 24 MAY 2014, DOI: 10.1016/j.fob.2014.05.003

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    Substantially elevating the levels of αB-crystallin in spinal motor neurons of mutant SOD1 mice does not significantly delay paralysis or attenuate mutant protein aggregation

    Journal of Neurochemistry

    Volume 133, Issue 3, May 2015, Pages: 452–464, Guilian Xu, Susan Fromholt, Jacob I. Ayers, Hilda Brown, Zoe Siemienski, Keith W. Crosby, Christopher A. Mayer, Christopher Janus and David R. Borchelt

    Version of Record online : 26 JAN 2015, DOI: 10.1111/jnc.13022

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    Protein charge ladders reveal that the net charge of ALS-linked superoxide dismutase can be different in sign and magnitude from predicted values

    Protein Science

    Volume 23, Issue 10, October 2014, Pages: 1417–1433, Yunhua Shi, Alireza Abdolvahabi and Bryan F. Shaw

    Version of Record online : 7 AUG 2014, DOI: 10.1002/pro.2526

  13. Targeting miR-155 restores abnormal microglia and attenuates disease in SOD1 mice

    Annals of Neurology

    Volume 77, Issue 1, January 2015, Pages: 75–99, Oleg Butovsky, Mark P. Jedrychowski, Ron Cialic, Susanne Krasemann, Gopal Murugaiyan, Zain Fanek, David J. Greco, Pauline M. Wu, Camille E. Doykan, Olga Kiner, Robert J. Lawson, Matthew P. Frosch, Nathalie Pochet, Rachid El Fatimy, Anna M. Krichevsky, Steven P. Gygi, Hans Lassmann, James Berry, Merit E. Cudkowicz and Howard L. Weiner

    Version of Record online : 27 NOV 2014, DOI: 10.1002/ana.24304

    Corrected by:

    Corrigendum: Corrigendum: Targeting miR-155 restores abnormal microglia and attenuates disease in SOD1 mice

    Vol. 77, Issue 6, 1085, Version of Record online: 22 APR 2015

  14. Extracellular aggregated Cu/Zn superoxide dismutase activates microglia to give a cytotoxic phenotype

    Glia

    Volume 61, Issue 3, March 2013, Pages: 409–419, Kate Roberts, Rafaa Zeineddine, Lisa Corcoran, Wen Li, Iain L. Campbell and Justin J. Yerbury

    Version of Record online : 22 DEC 2012, DOI: 10.1002/glia.22444

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    Abnormal exocytotic release of glutamate in a mouse model of amyotrophic lateral sclerosis

    Journal of Neurochemistry

    Volume 116, Issue 6, March 2011, Pages: 1028–1042, Marco Milanese, Simona Zappettini, Franco Onofri, Laura Musazzi, Daniela Tardito, Tiziana Bonifacino, Mirko Messa, Giorgio Racagni, Cesare Usai, Fabio Benfenati, Maurizio Popoli and Giambattista Bonanno

    Version of Record online : 20 JAN 2011, DOI: 10.1111/j.1471-4159.2010.07155.x

  16. A revisited folding reporter for quantitative assay of protein misfolding and aggregation in mammalian cells

    Biotechnology Journal

    Volume 7, Issue 10, October 2012, Pages: 1297–1307, Simpson Gregoire and Dr. Inchan Kwon

    Version of Record online : 27 JUN 2012, DOI: 10.1002/biot.201200103

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    Intracerebroventricular infusion of monoclonal antibody or its derived Fab fragment against misfolded forms of SOD1 mutant delays mortality in a mouse model of ALS

    Journal of Neurochemistry

    Volume 113, Issue 5, June 2010, Pages: 1188–1199, Francois Gros-Louis, Geneviève Soucy, Roxanne Larivière and Jean-Pierre Julien

    Version of Record online : 14 MAR 2010, DOI: 10.1111/j.1471-4159.2010.06683.x

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    Sequestosome 1/p62 links familial ALS mutant SOD1 to LC3 via an ubiquitin-independent mechanism

    Journal of Neurochemistry

    Volume 111, Issue 4, November 2009, Pages: 1062–1073, Jozsef Gal, Anna-Lena Ström, David M. Kwinter, Renée Kilty, Jiayu Zhang, Ping Shi, Weisi Fu, Marie W. Wooten and Haining Zhu

    Version of Record online : 18 SEP 2009, DOI: 10.1111/j.1471-4159.2009.06388.x

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    Characterization of Cu,Zn superoxide dismutase (SOD1) gene knock-out mutant of Cryptococcus neoformans var. gattii: role in biology and virulence

    Molecular Microbiology

    Volume 47, Issue 6, March 2003, Pages: 1681–1694, Srinivas D. Narasipura, Jeffrey G. Ault, Melissa J. Behr, Vishnu Chaturvedi and Sudha Chaturvedi

    Version of Record online : 5 MAR 2003, DOI: 10.1046/j.1365-2958.2003.03393.x

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    Selective mitochondrial Ca2+ uptake deficit in disease endstage vulnerable motoneurons of the SOD1G93A mouse model of amyotrophic lateral sclerosis

    The Journal of Physiology

    Volume 591, Issue 10, May 2013, Pages: 2723–2745, Andrea Fuchs, Sylvie Kutterer, Tobias Mühling, Johanna Duda, Burkhard Schütz, Birgit Liss, Bernhard U. Keller and Jochen Roeper

    Version of Record online : 12 MAR 2013, DOI: 10.1113/jphysiol.2012.247981