15. Interrupted Aortic Arch

  1. Constantine Mavroudis2,
  2. Carl Backer Associate Editor3 and
  3. Richid F. Idriss
  1. Richard A. Jonas

Published Online: 28 FEB 2013

DOI: 10.1002/9781118320754.ch15

Pediatric Cardiac Surgery, Fourth Edition

Pediatric Cardiac Surgery, Fourth Edition

How to Cite

Jonas, R. A. (2012) Interrupted Aortic Arch, in Pediatric Cardiac Surgery, Fourth Edition (eds C. Mavroudis, C. Backer and R. F. Idriss), Blackwell Publishing Ltd, Oxford, UK. doi: 10.1002/9781118320754.ch15

Editor Information

  1. 2

    Florida Hospital for Children, Orlando, FL, USA

  2. 3

    Ann & Robert H. Lurie Children's Hospital of Chicago, Chicago, IL, USA

Author Information

  1. Children's National Medical Center, Washington, DC, USA

Publication History

  1. Published Online: 28 FEB 2013
  2. Published Print: 28 DEC 2012

ISBN Information

Print ISBN: 9781405196529

Online ISBN: 9781118320754



  • pediatric;
  • interrupted aortic arch;
  • ventricular septal defect;
  • selective cerebral perfusion;
  • left ventricular outflow tract obstruction;
  • pressure gradient across arch;
  • DiGeorge syndrome;
  • left bronchial obstruction


This chapter covers interrupted aortic arch (IAA), starting with the anatomy and associated anomalies. Pathophysiology and clinical features are then covered. Diagnosis and management are discussed, including surgical techniques for interrupted arch and ventricular septal defect (VSD), selective cerebral perfusion, IAA with VSD and left ventricular outflow tract obstruction (LVOTO), and IAA with other anomalies. Postoperative management of IAA and complications of surgery such as pressure gradient across arch, LVOTO, DiGeorge syndrome, and left bronchial obstruction conclude the chapter.