7. The Branched-Chain Amino Acids: Leucine, Isoleucine and Valine

  1. David A Bender

Published Online: 2 JUL 2012

DOI: 10.1002/9781118357514.ch7

Amino Acid Metabolism, Third Edition

Amino Acid Metabolism, Third Edition

How to Cite

Bender, D. A. (2012) The Branched-Chain Amino Acids: Leucine, Isoleucine and Valine, in Amino Acid Metabolism, Third Edition, John Wiley & Sons, Ltd, Chichester, UK. doi: 10.1002/9781118357514.ch7

Author Information

  1. University College, London, UK

Publication History

  1. Published Online: 2 JUL 2012
  2. Published Print: 10 AUG 2012

ISBN Information

Print ISBN: 9780470661512

Online ISBN: 9781118357514

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Keywords:

  • branched-chain amino acids, leucine, isoleucine, valine;
  • leucine, isoleucine, valine, dietary for protein synthesis in animals;
  • bacteria, branched-chain oxo-acids, in branched-chain fatty acid synthesis;
  • common pathway of branched-chain amino acid synthesis;
  • isopropylmalate synthase and CoASH, feedback inhibition by leucine;
  • biotin in carboxylation, methylcrotonyl coA and propionyl CoA;
  • biotinidase, major plasma-binding protein for biotin;
  • genetic lack of biotinidase, variant of multiple carboxylase deficiency;
  • biotinidase in biotin tissue uptake

Summary

This chapter contains sections titled:

  • Synthesis of the branched-chain amino acids

  • Mammalian catabolism of the branched-chain amino acids

  • Further reading