12. Inherited Lung Disease in Children

  1. Janice Mighten RGN, RSCN, MSc, BMed Sci(Hons)
  1. Alan R. Smyth1,
  2. Ammani Prasad2 and
  3. Janice Mighten3

Published Online: 5 APR 2013

DOI: 10.1002/9781118702680.ch12

Children's Respiratory Nursing

Children's Respiratory Nursing

How to Cite

Smyth, A. R., Prasad, A. and Mighten, J. (2012) Inherited Lung Disease in Children, in Children's Respiratory Nursing (ed J. Mighten), John Wiley & Sons, Ltd,., West Sussex, UK. doi: 10.1002/9781118702680.ch12

Author Information

  1. 1

    Professor of Child Health, School of Clinical Sciences, University of Nottingham; Honorary Consultant in Paediatric Respiratory Medicine, Nottingham Children's Hospital

  2. 2

    CF Co-ordinatory/Senior Research Physiotherapist, Great Ormond Street Hospital for Children

  3. 3

    Children's Respiratory/Community Nurse Specialist, Nottingham Children's Hospital

Publication History

  1. Published Online: 5 APR 2013
  2. Published Print: 11 SEP 2012

ISBN Information

Print ISBN: 9781405197755

Online ISBN: 9781118702680



  • Active cycle of breathing techniques (ACBT);
  • Cystic fibrosis (CF);
  • Diagnosis;
  • Distal intestinal obstruction syndrome;
  • Home intravenous therapy;
  • Intrapulmonary percussive ventilation (IPV);
  • Lung disease;
  • Pathophysiology;
  • Physiotherapy;
  • Primary ciliary dyskinesia (PCD)


This chapter contains sections titled:

  • Primary Ciliary Dyskinesia

  • Cystic Fibrosis

  • Physiotherapy and Promoting Independence

  • Exercise

  • Physiotherapy Management of Babies and Young Children

  • Physiotherapy Management of Older Children and Teenagers

  • Nursing Management for Cystic Fibrosis

  • Care in the Community

  • Conclusion

  • References