Chapter 46. Pulmonary Atresia with Intact Ventricular Septum

  1. Julien I. E. Hoffman MD, FRCP Professor of Pediatrics (Emeritus) Senior Member

Published Online: 27 AUG 2009

DOI: 10.1002/9781444314045.ch46

The Natural and Unnatural History of Congenital Heart Disease

The Natural and Unnatural History of Congenital Heart Disease

How to Cite

Hoffman, J. I. E. (2009) Pulmonary Atresia with Intact Ventricular Septum, in The Natural and Unnatural History of Congenital Heart Disease, Wiley-Blackwell, Oxford, UK. doi: 10.1002/9781444314045.ch46

Author Information

  1. Cardiovascular Research Institute, Department of Pediatrics, University of California, San Francisco, CA, USA

Publication History

  1. Published Online: 27 AUG 2009
  2. Published Print: 28 AUG 2009

ISBN Information

Print ISBN: 9781405179270

Online ISBN: 9781444314045

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Keywords:

  • pulmonary atresia with intact ventricular septum;
  • pulmonary valve imperforate;
  • imperforate pulmonary valve and intact ventricular septum;
  • main and branch pulmonary arteries - hypoplastic;
  • aorta wide and normal and isthmic narrowing absent;
  • patency of ductus arteriosus and flow to lungs control;
  • fetal diagnosis and outcome prediction;
  • pulmonary blood flow and aortopulmonary shunt;
  • severely hypoplastic right ventricle

Summary

This chapter contains sections titled:

  • Pathological anatomy

  • Pathophysiology

  • Natural history

  • Unnatural history

  • References