Chapter 16. Intracranial Granulomatous Arteritis (Primary Angiitis of the CNS)/Idiopathic CNS Vasculitis

  1. Robert P. Lisak MD, FAAN, FRCP Parker Webber Chair Professor Chair Neurologist-in-Chief Chief2,3,
  2. Daniel D. Truong MD, FAAN Head4,
  3. William M. Carroll MBBS, MD, FRACP, FRCP(E) Head5 and
  4. Roongroj Bhidayasiri MD, FRCP Director6,7
  1. Donald Silberberg MD Professor of Neurology

Published Online: 18 MAY 2010

DOI: 10.1002/9781444317008.ch16

International Neurology: A Clinical Approach

International Neurology: A Clinical Approach

How to Cite

Silberberg, D. (2009) Intracranial Granulomatous Arteritis (Primary Angiitis of the CNS)/Idiopathic CNS Vasculitis, in International Neurology: A Clinical Approach (eds R. P. Lisak, D. D. Truong, W. M. Carroll and R. Bhidayasiri), Wiley-Blackwell, Oxford, UK. doi: 10.1002/9781444317008.ch16

Editor Information

  1. 2

    Wayne State University School of Medicine, Detroit, MI, USA

  2. 3

    Detroit Medical Center, Harper University Hospital, Detroit, MI, USA

  3. 4

    The Parkinson and Movement Disorder Institute, Memorial Neuroscience Institute, Orange Coast Memorial Medical Center, Fountain Valley, CA, USA

  4. 5

    Sir Charles Gairdner Hospital, Nedlands, Perth, Australia

  5. 6

    Chulalongkorn Comprehensive Movement Disorders Center, Chulalongkorn University Hospital, Bangkok, Thailand

  6. 7

    University of California at Los Angeles, School of Medicine, Los Angeles, CA, USA

Author Information

  1. Department of Neurology, University of Pennsylvania Medical Center, Philadelphia, PA, USA

Publication History

  1. Published Online: 18 MAY 2010
  2. Published Print: 11 SEP 2009

ISBN Information

Print ISBN: 9781405157384

Online ISBN: 9781444317008

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Keywords:

  • intracranial granulomatous arteritis - CNS primary angiitis;
  • ICNSV - idiopathic CNS vasculitis;
  • diagnosis and clinical course - elevated peripheral blood leukocyte count;
  • perivascular inflammation revealing - brain and meningeal biopsy;
  • ICNSV treatment - azathioprine;
  • treatment efficiency and clinical response;
  • synthetic corticosteroids and immunosuppressant - reducing disease severity

Summary

This chapter contains sections titled:

  • Nomenclature

  • Diagnosis and clinical course

  • Treatment

  • Future developments

  • Further reading