Chapter 60. Scapuloperoneal Syndrome

  1. Robert P. Lisak MD, FAAN, FRCP Parker Webber Chair Professor Chair Neurologist-in-Chief Chief4,5,
  2. Daniel D. Truong MD, FAAN Head6,
  3. William M. Carroll MBBS, MD, FRACP, FRCP(E) Head7 and
  4. Roongroj Bhidayasiri MD, FRCP Director8,9
  1. Georges Serratrice FRCP Emeritus Professor of Neurology Head Past President1,2,3

Published Online: 18 MAY 2010

DOI: 10.1002/9781444317008.ch60

International Neurology: A Clinical Approach

International Neurology: A Clinical Approach

How to Cite

Serratrice, G. (2009) Scapuloperoneal Syndrome, in International Neurology: A Clinical Approach (eds R. P. Lisak, D. D. Truong, W. M. Carroll and R. Bhidayasiri), Wiley-Blackwell, Oxford, UK. doi: 10.1002/9781444317008.ch60

Editor Information

  1. 4

    Wayne State University School of Medicine, Detroit, MI, USA

  2. 5

    Detroit Medical Center, Harper University Hospital, Detroit, MI, USA

  3. 6

    The Parkinson and Movement Disorder Institute, Memorial Neuroscience Institute, Orange Coast Memorial Medical Center, Fountain Valley, CA, USA

  4. 7

    Sir Charles Gairdner Hospital, Nedlands, Perth, Australia

  5. 8

    Chulalongkorn Comprehensive Movement Disorders Center, Chulalongkorn University Hospital, Bangkok, Thailand

  6. 9

    University of California at Los Angeles, School of Medicine, Los Angeles, CA, USA

Author Information

  1. 1

    Department of Neurology, Timone Hospital, Marseille, France

  2. 2

    Aix-Marseille University, France

  3. 3

    French Society of Neurology, France

Publication History

  1. Published Online: 18 MAY 2010
  2. Published Print: 11 SEP 2009

ISBN Information

Print ISBN: 9781405157384

Online ISBN: 9781444317008



  • scapuloperoneal syndrome, defined by localized weakness and atrophy of shoulder girdle muscles;
  • nosology of cases reported - under this heading remaining uncertain;
  • neuromuscular diseases, presenting with scapuloperoneal distribution of muscle weakness;
  • humeral muscles in Emery–Dreifuss muscular dystrophy;
  • scapuloperoneal muscular dystrophy;
  • serum CK activity, slightly to moderately elevated - electromyography (EMG) showing a myopathic pattern;
  • scapuloperoneal neuropathy, called Dawidenkow type - rare disease characterized by autosomal dominant inheritance;
  • Emery–Dreifuss muscular dystrophy


This chapter contains sections titled:

  • Introduction

  • Clinical features

  • Treatment/management

  • Further reading