141. Disorders of Fat Tissue

  1. Alan D. Irvine MD, FRCPI, FRCP2,3,
  2. Peter H. Hoeger MD4,5 and
  3. Albert C. Yan MD, FAAP, FAAD6,7
  1. Marc Lacour

Published Online: 24 MAY 2011

DOI: 10.1002/9781444345384.ch141

Harper's Textbook of Pediatric Dermatology, Volume 1, 2, Third Edition

Harper's Textbook of Pediatric Dermatology, Volume 1, 2, Third Edition

How to Cite

Lacour, M. (2011) Disorders of Fat Tissue, in Harper's Textbook of Pediatric Dermatology, Volume 1, 2, Third Edition (eds A. D. Irvine, P. H. Hoeger and A. C. Yan), Wiley-Blackwell, Oxford, UK. doi: 10.1002/9781444345384.ch141

Editor Information

  1. 2

    Trinity College, Dublin, Ireland

  2. 3

    Our Lady's Children's Hospital, Dublin, Ireland

  3. 4

    University of Hamburg, Hamburg, Germany

  4. 5

    Catholic Children's Hospital Wilhelmstift, Hamburg, Germany

  5. 6

    University of Pennsylvania School of Medicine, Philadelphia, PA, USA

  6. 7

    The Children's Hospital of Philadelphia, Philadelphia, PA, USA

Author Information

  1. Swiss Group for Pediatric Dermatology, Geneva, Switzerland

Publication History

  1. Published Online: 24 MAY 2011
  2. Published Print: 3 JUN 2011

ISBN Information

Print ISBN: 9781405176958

Online ISBN: 9781444345384

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Keywords:

  • hibernoma;
  • lipoatrophy;
  • lipoblastoma;
  • lipodystrophy;
  • lipohypertrophy;
  • lipoma;
  • lipomatoses;
  • obesity

Summary

This chapter is a comprehensive review of non-inflammatory disorders of fat tissue. The first part describes lipohypertrophic disorders, further separated INTO inherited or acquired disorders. It includes localized entities such as lipomas, hibernomas, disorders with more widespread fat hypertrophy such as lipomatoses and PTEN hamartoma tumour syndromes, and lastly monogenic conditions leading to generalized fat hypertrophy (obesity), such as Prader–WillI or Alström's syndrome. The second part of the chapter describes lipoatrophic disorders which are presented in a similar manner as localized, partial and generalized forms of lipoatrophy. Disorders presenting in childhood, such as centrifugal lipoatrophy and congenital lipodystrophies, are emphasized.