167. Wegener Granulomatosis, Polyarteritis Nodosa, Microscopic Polyangiitis, Behçet Disease and Relapsing Polychondritis

  1. Alan D. Irvine MD, FRCPI, FRCP3,4,
  2. Peter H. Hoeger MD5,6 and
  3. Albert C. Yan MD, FAAP, FAAD7,8
  1. Paul A. Brogan BSc (Hon), MBChB (Hon), FRCPCH, MSc, PhD1 and
  2. Jane Tizard2

Published Online: 24 MAY 2011

DOI: 10.1002/9781444345384.ch167

Harper's Textbook of Pediatric Dermatology, Volume 1, 2, Third Edition

Harper's Textbook of Pediatric Dermatology, Volume 1, 2, Third Edition

How to Cite

Brogan, P. A. and Tizard, J. (2011) Wegener Granulomatosis, Polyarteritis Nodosa, Microscopic Polyangiitis, Behçet Disease and Relapsing Polychondritis, in Harper's Textbook of Pediatric Dermatology, Volume 1, 2, Third Edition (eds A. D. Irvine, P. H. Hoeger and A. C. Yan), Wiley-Blackwell, Oxford, UK. doi: 10.1002/9781444345384.ch167

Editor Information

  1. 3

    Trinity College, Dublin, Ireland

  2. 4

    Our Lady's Children's Hospital, Dublin, Ireland

  3. 5

    University of Hamburg, Hamburg, Germany

  4. 6

    Catholic Children's Hospital Wilhelmstift, Hamburg, Germany

  5. 7

    University of Pennsylvania School of Medicine, Philadelphia, PA, USA

  6. 8

    The Children's Hospital of Philadelphia, Philadelphia, PA, USA

Author Information

  1. 1

    Institute of Child Health, University College London, London, UK

  2. 2

    Bristol Royal Hospital for Children Bristol, UK

Publication History

  1. Published Online: 24 MAY 2011
  2. Published Print: 3 JUN 2011

ISBN Information

Print ISBN: 9781405176958

Online ISBN: 9781444345384

SEARCH

Keywords:

  • Wegener granulomatosis (WG), antineutrophil cytoplasmic antibody (ANCA) - associated vasculitides (AAV);
  • WG, and the Chapel Hill criteria - granulomatous inflammation in respiratory tract;
  • sensitivity and specificity - new EULAR/PRINTO/PRES criteria;
  • ANCA generation aetiology - in WG, unknown;
  • WG, necrotizing granulomatous vasculitis - affecting arteries and veins;
  • coronary arteritis, myocardial infarction - aortic or mitral valves;
  • microscopic polyangiitis (MPA, earlier as microscopic polyarteritis) - differs from classic PAN;
  • Behçet disease (BD), and Halusi Behçet - a Turkish dermatologist (1937);
  • EULAR 2008 recommendations - treatment of Behçet disease;
  • European League against Rheumatism (EULAR) - treatment of adults with Behcet disease

Summary

This chapter contains sections titled:

  • Wegener granulomatosis

  • Polyarteritis nodosa and microscopic polyangiitis

  • Behçet disease

  • Relapsing polychondritis

  • References