13. Budd-Chiari Syndrome – Hepatic Venous Outflow Tract Obstruction

  1. Roberto de Franchis MD, AGAF Professor of Gastroenterology Head
  1. Dominique-Charles Valla MD Professeur Chef

Published Online: 17 NOV 2010

DOI: 10.1002/9781444393989.ch13

Portal Hypertension V: Proceedings of the Fifth Baveno International Consensus Workshop, Fifth Edition

Portal Hypertension V: Proceedings of the Fifth Baveno International Consensus Workshop, Fifth Edition

How to Cite

Valla, D.-C. (2011) Budd-Chiari Syndrome – Hepatic Venous Outflow Tract Obstruction, in Portal Hypertension V: Proceedings of the Fifth Baveno International Consensus Workshop, Fifth Edition (ed R. de Franchis), Wiley-Blackwell, Oxford, UK. doi: 10.1002/9781444393989.ch13

Editor Information

  1. Department of Medical Sciences, University of Milan, and Gastroenterology 3 Unit, IRCCS Ca' Granda Ospedale Maggiore Policlinico Mangiagalli and Regina Elena Foundation, Milan, Italy

Author Information

  1. Department of Hepatology, Hôpital Beaujon, AP-HP, Université Denis Diderot-Paris 7, and Inserm U773, Clichy, France

Publication History

  1. Published Online: 17 NOV 2010
  2. Published Print: 14 JAN 2011

ISBN Information

Print ISBN: 9781444334494

Online ISBN: 9781444393989

SEARCH

Keywords:

  • vascular disease of liver, Budd-Chiari Syndrome - hepatic venous outflow tract obstruction;
  • Baveno IV workshop, on patient management - with primary Budd-Chiari syndrome (BCS)/hepatic venous outflow tract obstruction (HVOTO);
  • primary Budd-Chiari syndrome - and causal factors;
  • JAK2 V617F somatic mutation detection - in peripheral blood, myeloproliferative disease (MPD) diagnosis;
  • portal vein thrombosis - affecting 10–20% of BCS patients;
  • chronic obstruction of terminal IVC - associated with hepatocellular carcinoma;
  • Baveno IV consensus statements - emphasizing non-invasive imaging, and HVOTO demonstration;
  • data on specific therapy - for underlying disease in context of BCS, still awaited;
  • area under the receiver operating characteristic curve (AUROC);
  • MPD, and severe BCS - at presentation, with a shorter time to invasive therapy

Summary

This chapter contains sections titled:

  • Introduction

  • Epidemiology

  • Causal factors for primary Budd-Chiari syndrome

  • Manifestations

  • Diagnosis

  • Therapy

  • Prognosis

  • References