13. Budd-Chiari Syndrome – Hepatic Venous Outflow Tract Obstruction
- Roberto de Franchis MD, AGAF Professor of Gastroenterology Head
Published Online: 17 NOV 2010
DOI: 10.1002/9781444393989.ch13
Copyright © 2011 Blackwell Publishing Ltd
Book Title
Portal Hypertension V: Proceedings of the Fifth Baveno International Consensus Workshop, Fifth Edition
Additional Information
How to Cite
Valla, D.-C. (2011) Budd-Chiari Syndrome – Hepatic Venous Outflow Tract Obstruction, in Portal Hypertension V: Proceedings of the Fifth Baveno International Consensus Workshop, Fifth Edition (ed R. de Franchis), Wiley-Blackwell, Oxford, UK. doi: 10.1002/9781444393989.ch13
Editor Information
Department of Medical Sciences, University of Milan, and Gastroenterology 3 Unit, IRCCS Ca' Granda Ospedale Maggiore Policlinico Mangiagalli and Regina Elena Foundation, Milan, Italy
Publication History
- Published Online: 17 NOV 2010
- Published Print: 14 JAN 2011
ISBN Information
Print ISBN: 9781444334494
Online ISBN: 9781444393989
- Summary
- Chapter
- References
Keywords:
- vascular disease of liver, Budd-Chiari Syndrome - hepatic venous outflow tract obstruction;
- Baveno IV workshop, on patient management - with primary Budd-Chiari syndrome (BCS)/hepatic venous outflow tract obstruction (HVOTO);
- primary Budd-Chiari syndrome - and causal factors;
- JAK2 V617F somatic mutation detection - in peripheral blood, myeloproliferative disease (MPD) diagnosis;
- portal vein thrombosis - affecting 10–20% of BCS patients;
- chronic obstruction of terminal IVC - associated with hepatocellular carcinoma;
- Baveno IV consensus statements - emphasizing non-invasive imaging, and HVOTO demonstration;
- data on specific therapy - for underlying disease in context of BCS, still awaited;
- area under the receiver operating characteristic curve (AUROC);
- MPD, and severe BCS - at presentation, with a shorter time to invasive therapy
Summary
This chapter contains sections titled:
Introduction
Epidemiology
Causal factors for primary Budd-Chiari syndrome
Manifestations
Diagnosis
Therapy
Prognosis
References