Cor triatriatum

An unusual cause of elevated pulmonary capillary wedge pressure in a child with tetralogy of fallot


  • Conflict of interest: Nothing to report.

Correspondence to: Dr. Saurabh Kumar Gupta, MD, DM, Assistant Professor, Department of Cardiology, Room No. 23, 7th floor, CN Centre, All India Institute of Medical Sciences, Ansari Nagar, New Delhi 110029, India. E-mail:


The coexistence of cor triatriatum and tetralogy of Fallot (TOF) is rare. Preoperative identification of cor triatriatum may be difficult owing to reduced pulmonary blood flow in patients with TOF. However, it is imperative to identify this rare combination as failure to identify obstruction to pulmonary venous egress may result in persistent pulmonary venous hypertension postoperatively. The authors discuss hemodynamic aspects of this rare coexistence in a 14-month-old child in whom pulmonary capillary wedge pressure was elevated despite right ventricular outflow obstruction. © 2012 Wiley Periodicals, Inc.