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Malignant phosphaturic mesenchymal tumor of the larynx§


  • This study was presented as a poster at the Triological Society Combined Sections Meeting, Scottsdale, AZ, January 27–29, 2011.

  • The authors have no financial disclosures for this article.

  • §

    The authors have no conflicts of interest to declare.


Phosphaturic mesenchymal tumors are rare neoplasms predominantly originating in the trunk and extremities. Malignant variants are exceedingly rare, and can present significant diagnostic challenges to the pathologist and otolaryngologist alike. This report describes the first case of malignant phosphaturic mesenchymal tumor involving the larynx, and emphasizes the importance of vigilance in both histopathologic and clinical actions so that appropriate treatment can be provided in a timely manner. The clinical presentation, radiologic and histologic features, and management are discussed.