The authors have no funding, financial relationships, or conflicts of interest to disclose.
Version of Record online: 6 SEP 2011
Copyright © 2011 The American Laryngological, Rhinological, and Otological Society, Inc.
Volume 121, Issue 10, pages 2256–2261, October 2011
How to Cite
Lee, G. S., Zhou, G., Poe, D., Kenna, M., Amin, M., Ohlms, L. and Gopen, Q. (2011), Clinical experience in diagnosis and management of superior semicircular canal dehiscence in children. The Laryngoscope, 121: 2256–2261. doi: 10.1002/lary.22134
This study was presented at the Combined Otolaryngological Spring Meeting, American Otological Society, Las Vegas, Nevada, April 28 – May 2, 2010.
- Issue online: 21 SEP 2011
- Version of Record online: 6 SEP 2011
- Manuscript Accepted: 3 MAY 2011
- Manuscript Revised: 26 APR 2011
- Manuscript Received: 14 DEC 2010
- Semicircular canal dehiscence;
- pediatric hearing loss;
- vestibular dysfunction;
- VEMP testing;
- Level of Evidence: 4
To identify clinical characteristics of pediatric superior semicircular canal dehiscence (SSCD) and explore suitable options of management.
The study comprised 10 patients with auditory and/or vestibular symptoms suspicious for SSCD. One patient pursued care at another institution, and two did not return for follow-up. Subsequently, seven patients (11 ears, 6 females and 1 male, aged 5–11 years) were included. Patients were evaluated using high-resolution temporal bone computed tomography. Those suspected of having SSCD underwent vestibular evoked myogenic potential testing for confirmation in addition to routine audiologic tests.
All seven patients had auditory and/or vestibular impairment. Auditory symptoms included autophony, tinnitus, and conductive or mixed hearing loss. Bone conduction responses were occasionally better than 0 dB HL. Vestibular dysfunction included vertigo, often in response to loud noises, and chronic disequilibrium. One patient underwent surgical repair for disabling vestibular symptoms with dramatic improvement in both auditory and vestibular symptoms postoperatively. The remaining six were closely monitored with routine exams.
In contrast to adults, children with SSCD usually present with auditory symptoms first, although they share some similarities with adults in clinical manifestations of SSCD. Our study shows that SSCD syndrome, a well-accepted clinical entity, exists in the pediatric population. Conservative management is preferred for children with SSCD; nevertheless, surgical intervention is necessary for those with disabling vestibular symptoms. To date, this is the first clinical case series of symptomatic pediatric patients with SSCD.