The authors have no funding, financial relationships, or conflicts of interest to disclose.
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Otology/Neurotology
Endolymphatic sac tumor and angiomatous lesions of the nasal and pharyngeal mucosa as a first manifestation of von Hippel-Lindau disease†
Article first published online: 9 JUL 2012
DOI: 10.1002/lary.23438
Copyright © 2012 The American Laryngological, Rhinological, and Otological Society, Inc.
Additional Information
How to Cite
Honeder, C., Gstoettner, W., Matula, C., Czerny, C., Gruber, A., Ramsebner, R. and Arnoldner, C. (2012), Endolymphatic sac tumor and angiomatous lesions of the nasal and pharyngeal mucosa as a first manifestation of von Hippel-Lindau disease. The Laryngoscope, 122: 2300–2303. doi: 10.1002/lary.23438
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Publication History
- Issue published online: 20 SEP 2012
- Article first published online: 9 JUL 2012
- Manuscript Accepted: 25 APR 2012
- Manuscript Revised: 17 APR 2012
- Manuscript Received: 18 MAR 2012
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Keywords:
- Endolymphatic sac tumor;
- von Hippel-Lindau disease;
- angiomatous lesions
Abstract
In the present article we report an endolymphatic sac tumor in a 15-year-old male who had additional angiomatous lesions in the nasal and pharyngeal mucosa and was diagnosed with von Hippel-Lindau disease postoperatively. Preoperative imaging excluded cholesteatoma, but did not provide sufficient information to distinguish between jugular paraganglioma and endolymphatic sac tumor. To the authors' knowledge this is the first description of angiomatous lesions in the mucosa of the upper respiratory tract in a von Hippel-Lindau disease patient, a potentially useful finding for future radiological differential diagnosis in cases presenting with endolymphatic sac tumor. Laryngoscope, 2012