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Hemichorea as an initial manifestation of moyamoya disease: Reversible striatal hypoperfusion demonstrated on single photon emission computed tomography

Authors

  • Yoon-Ho Hong MD,

    1. Department of Neurology, Clinical Research Institute, Seoul National University Hospital, SNUMRC, College of Medicine, Seoul National University, Seoul, South Korea
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  • Tae-Beom Ahn MD,

    1. Department of Neurology, Clinical Research Institute, Seoul National University Hospital, SNUMRC, College of Medicine, Seoul National University, Seoul, South Korea
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  • Chang Wan Oh MD,

    1. Department of Neurosurgery, Clinical Research Institute, Seoul National University Hospital, SNUMRC, College of Medicine, Seoul National University, Seoul, South Korea
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  • Beom S. Jeon MD, PhD

    Corresponding author
    1. Department of Neurology, Clinical Research Institute, Seoul National University Hospital, SNUMRC, College of Medicine, Seoul National University, Seoul, South Korea
    • Department of Neurology, Seoul National University Hospital, 28 Yongon-Dong Chongno-gu, Seoul, 110-744, South Korea
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Abstract

We describe a case with unilateral moyamoya disease that showed progressive hemichorea as an initial manifestation. Single photon emission computed tomography showed perfusion defect in the contralateral basal ganglia although magnetic resonance imaging was unremarkable. Hemichorea improved along with normalization of perfusion after bypass surgery, suggestive of striatal hypoperfusion as the cause of hemichorea. © 2002 Movement Disorder Society

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