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Keywords:

  • Creutzfeldt–Jakob;
  • magnetic resonance imaging;
  • alien limb;
  • video;
  • corticobasal degeneration

Abstract

Creutzfeldt–Jakob disease is a fatal spongiform encephalopathy, which typically presents with a rapidly progressing dementia and additional neurological findings that can be quite variable and diverse. Here we report the unusual case of a patient who presented with left alien limb sign without overt cognitive impairment and was ultimately diagnosed with pathologically confirmed Creutzfeldt–Jakob disease. © 2006 Movement Disorder Society