The treatment of scoliosis in duchenne muscular dystrophy
Article first published online: 13 OCT 2004
Copyright © 1984 John Wiley & Sons, Inc.
Muscle & Nerve
Volume 7, Issue 4, pages 281–286, May 1984
How to Cite
Rideau, Y., Glorion, B., Delaubier, A., Tarlé, O. and Bach, J. (1984), The treatment of scoliosis in duchenne muscular dystrophy. Muscle Nerve, 7: 281–286. doi: 10.1002/mus.880070405
- Issue published online: 13 OCT 2004
- Article first published online: 13 OCT 2004
- Manuscript Revised: 3 NOV 1983
- Manuscript Received: 15 APR 1983
There are not, as yet, clear indications for the surgical management of scoliosis in Duchenne muscular dystrophy (DMD), taking into account the varying severity of the clinical course. Monitoring the vital capacity can be most important for the indication and timing of surgery. In some cases, delaying surgical intervention with conservative management using spinal braces and wheelchair inserts can permit the restrictive lung syndrome to advance to the point that surgery will be contraidicated. Ten such patients conservatively treated for an average of 5 years exhibited perhaps a slower progression but ultimately an advanced deformity. From a second group of five carefully selected and surgically treated patients, indications for spinal surgery were reviewed. Surgical intervention should be prophylatically undertaken when there is high risk of a rapidly evolving curve with a severe restrictive lung syndrome.