The authors declare that there is no disclosure and any conflict of interest.
Successful radiation therapy for supratentorial primitive neuroectodermal tumor and epidermolysis bullosa simplex†
Article first published online: 16 SEP 2009
Copyright © 2009 Wiley-Liss, Inc.
Pediatric Blood & Cancer
Volume 54, Issue 1, pages 170–172, January 2010
How to Cite
Bavishi, S., Wong, K., Delgardo, T., Marachelian, A. and Khatua, S. (2010), Successful radiation therapy for supratentorial primitive neuroectodermal tumor and epidermolysis bullosa simplex. Pediatr. Blood Cancer, 54: 170–172. doi: 10.1002/pbc.22281
- Issue published online: 9 NOV 2009
- Article first published online: 16 SEP 2009
- Manuscript Accepted: 12 AUG 2009
- Manuscript Received: 27 JUL 2009
- epidermolysis bullosa simplex;
- radiation therapy;
- supratentorial PNET
Epidermolysis bullosa simplex (EBS) is a heritable skin disorder characterized by skin fragility and blistering. While its most severe variant, dystrophic epidermolysis bullosa (DEB) is associated with squamous cell carcinoma (SCC), the development of extracutaneous neoplasms in EBS is extremely rare. We report a novel case of supratentorial primitive neuroectodermal tumor (sPNET) in a 7-year male with EBS. Experience of radiation therapy and its challenges in children with EBS has rarely been reported. Pediatr Blood Cancer 2010; 54:170–172. © 2009 Wiley-Liss, Inc.