C Mas, MD, Paediatric Cardiology Fellow. DJ Penny, MD, MRCP, Paediatric Cardiology Fellow. S Menahem, MD, MEd, MPM, FRACP, FACC, Head, Paediatric Cardiology Unit. Current addresses: C Mas, Hospital Nal de Ninos, San Jose, Costa Rica. DJ Penny, Paediatric Intensive Care, Great Ormond Street Hospital for Children NHS Trust, Great Ormond Street, London WC1N 3JH, United Kingdom.
Pre-excitation syndrome secondary to cardiac rhabdomyomas in tuberous sclerosis
Article first published online: 24 DEC 2001
Journal of Paediatrics and Child Health
Volume 36, Issue 1, pages 84–86, February 2000
How to Cite
Mas, C., Penny, D. and Menahem, S. (2000), Pre-excitation syndrome secondary to cardiac rhabdomyomas in tuberous sclerosis. Journal of Paediatrics and Child Health, 36: 84–86. doi: 10.1046/j.1440-1754.2000.00443.x
- Issue published online: 24 DEC 2001
- Article first published online: 24 DEC 2001
- hydrops fetalis;
- pre-excitation syndrome;
- supraventricular tachycardia;
- tuberous sclerosis
Abstract: Rhabdomyomas are not uncommon in infants with tuberous sclerosis. We describe a neonate who presented with hydrops fetalis arising from a tachyarrhythmia during fetal life related to rhabdomyomas. After reversion of the arrhythmia, pre-excitation was noted on an interval electrocardiogram. Following regression of the tumours, the delta wave disappeared with no further arrhythmias noted.