Pseudo-maple syrup urine disease due to maternal prenatal ingestion of fenugreek

Authors


Correspondence: DrSKorman, Department of Clinical Biochemistry, Hadassah University Hospital, PO Box 12000, Jerusalem 91120, Israel. Fax: +972 2-6435778; email: korman@hadassah.org.il

Abstract

Abstract: Fenugreek, maple syrup and the urine of maple syrup urine disease (MSUD) patients all share a characteristic odour originating from a common component, sotolone. Ingestion of fenugreek by mothers during labour resulted in a maple syrup-like odour in their newborn infants, leading to a false suspicion of MSUD.

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