We are grateful to Dr. V. Jackson-Lewis for assisting in the tissue sample preparation, to Dr. A. B. Naini for performing the SOD1 assays, and to Drs. M. Gurney and T. Siddique for providing the G1H mice used in this work. This study was supported by the Muscular Dystrophy Association, Project-ALS, the National Institute of Neurological Disorders and Stroke grant (R29 NS37345), the Lowenstein Foundation, the Smart Foundation, and the Parkinson's Disease Foundation. G.A. is a recipient of the Erwin Schrödinger Scholarship of the Austrian Research Funds, and S.P. is a recipient of the Cotzias Award from the American Parkinson Disease Association.

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