We are grateful to M. Righi and G. Rossi for technical help. This work was supported by the INFM (Sez. B), Consiglio Nazionale delle Ricerche (PF Biotecnologie), TeleThon (grant E. 1044 to A.C.), SIRS srl, and by grant 75195-54701 from Howard Hughes Medical Institute awarded to A.C. and M.N. L.F. acknowledges a fellowship from SIRS srl.

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