Use of an Insertable Loop Recorder in a Myotonic Dystrophy Patient

Authors


  • This work was supported by grants from Medtronic, Inc., Minneapolis, Minnesota; the Muscular Dystrophy Association, Tucson, Arizona; and the National Institute of Health Grant MO1-RR00750-27S1.

  • This manuscript was processed by a guest editor.

Address for correspondence: William J. Groh, M.D., Krannert Institute of Cardiology, Indiana University School of Medicine, 1111West 10th Street, KI 316, Indianapolis, IN 46202-4800. Fax: 317-656-4140; E-mail wgroh@iupui.edu

Abstract

Loop Recorder Use in Myotonic Dystrophy. The case of a 66-year-old woman with myotonic dystrophy is presented. This patient underwent implantation of an insertable loop recorder as a participant in a clinical trial. At 1-month follow-up, interrogation of the insertable loop recorder revealed multiple episodes of wide complex tachycardia. She underwent electrophysiologic study, which revealed moderate His-Purkinje disease, focal atrial tachycardia, monomorphic ventricular tachycardia, and ventricular fibrillation. Successful radiofrequency ablation of the focal atrial tachycardia and implantation of a dual-chamber implantable cardioverter defibrillator was performed.

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