This work was supported in part by National Institutes of Health- National Institute on Deafness and Other Communication Disorders Grant P30 DC4660, the Lions International of Minnesota, and the International Hearing Foundation.
Temporal Bone Study of Trisomy 13 Syndrome†
Article first published online: 2 JAN 2009
Copyright © 2008 The Triological Society
Volume 118, Issue 3, pages 506–507, March 2008
How to Cite
Fukushima, H., Schachern, P. A., Cureoglu, S. and Paparella, M. M. (2008), Temporal Bone Study of Trisomy 13 Syndrome. The Laryngoscope, 118: 506–507. doi: 10.1097/MLG.0b013e31815b2176
- Issue published online: 2 JAN 2009
- Article first published online: 2 JAN 2009
- Manuscript Accepted: 13 SEP 2007
- Trisomy 13 syndrome;
- human temporal bone;
The temporal bones of a 23-week-old female who had multiple congenital anomalies and bilateral hearing loss with trisomy 13 syndrome were evaluated under light microscopy.
In the left cochlea, spiral ganglion cells and cochlear nerve fibers are absent. In the right ear, an abnormal branch of the singular nerve passes between the utricle and lateral semicircular canals and separates the two portions, one to the flattened crista of the lateral semicircular canal, the other to the utricular macula. This is a rare report describing a patient with abnormalities in three nerves, including the facial, vestibular, and cochlear nerves.