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Palmoplantar contractures in childhood: a rare complication of vascular Ehlers–Danlos syndrome

Authors


  • Conflict of interest: none declared.

Correspondence: Dr Amy C. Foulkes, The Dermatology Centre, The University of Manchester, Salford Royal NHS Foundation Trust, Manchester Academic Health Science Centre, M6 8HD, UK

E-mail: amy.foulkes@manchester.ac.uk

Summary

Although catastrophic vascular complications in vascular Ehlers–Danlos Syndrome (EDS) are well recognized, other complications such as flexion contractures and tendon nodules are rarely reported and poorly characterized. We report a young man with vascular EDS, who developed flexion contractures and tendon nodules, causing considerable disability. Limited management strategies are available for these complications, which have continued to prove a challenge to management.

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