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Palmoplantar contractures in childhood: a rare complication of vascular Ehlers–Danlos syndrome


  • Conflict of interest: none declared.

Correspondence: Dr Amy C. Foulkes, The Dermatology Centre, The University of Manchester, Salford Royal NHS Foundation Trust, Manchester Academic Health Science Centre, M6 8HD, UK



Although catastrophic vascular complications in vascular Ehlers–Danlos Syndrome (EDS) are well recognized, other complications such as flexion contractures and tendon nodules are rarely reported and poorly characterized. We report a young man with vascular EDS, who developed flexion contractures and tendon nodules, causing considerable disability. Limited management strategies are available for these complications, which have continued to prove a challenge to management.