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Maffucci syndrome with the spindle cell hemangiomas in the mucosa of the lower lip: a rare case report and literature review

Authors

  • Yu Cai,

    1. Department of Oral and Maxillofacial Surgery, School and Hospital of Stomatology, Wuhan University, Wuhan, P. R. China
    2. The State Key Laboratory Breeding Base of Basic Science of Stomatology (Hubei-MOST) & Key Laboratory of Oral Biomedical Engineering of Ministry of Education, School & Hospital of Stomatology, Wuhan University, Wuhan, P. R. China
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  • Rong Wang,

    1. The State Key Laboratory Breeding Base of Basic Science of Stomatology (Hubei-MOST) & Key Laboratory of Oral Biomedical Engineering of Ministry of Education, School & Hospital of Stomatology, Wuhan University, Wuhan, P. R. China
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  • Xin-Ming Chen,

    1. Department of Oral Pathology, School and Hospital of Stomatology, Wuhan University, Wuhan, P. R. China
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  • Yi-Fang Zhao,

    1. Department of Oral and Maxillofacial Surgery, School and Hospital of Stomatology, Wuhan University, Wuhan, P. R. China
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  • Zhi-Jun Sun,

    1. Department of Oral and Maxillofacial Surgery, School and Hospital of Stomatology, Wuhan University, Wuhan, P. R. China
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  • Ji-Hong Zhao

    Corresponding author
    • Department of Oral and Maxillofacial Surgery, School and Hospital of Stomatology, Wuhan University, Wuhan, P. R. China
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  • Yu Cai and Rong Wang contributed equally to this work.

Ji-Hong Zhao

Department of Oral and Maxillofacial Surgery, School and Hospital of Stomatology, Wuhan University, 237 LuoYu Road, Wuhan 430079, P. R. China

Tel: +86 27 87686214

Fax: +86 27 87873260

e-mail: jhzhao988@yahoo.com.cn

Abstract

The presence of non-cutaneous vascular lesions in the syndrome of multiple enchondromas and subcutaneous hemangiomas, also named Maffucci syndrome, is exceedingly rare. Until now, non-cutaneous vascular lesions have been described in nine patients, while only three cases were present in the oral cavity; they were found in the tongue in two patients and in the lower lip in one patient. Herein, we report the second case of vascular lesions localized in the mucosa of lower lip in a patient with Maffucci syndrome. Histopathologic examination showed spindle cell hemangioma.

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