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Type III Sturge-Weber Syndrome With Migraine-Like Attacks Associated With Prolonged Visual Aura

Authors

  • Hung Yu Huang MD,

    1. Neuroscience Laboratory, Department of Neurology, China Medical University Hospital, Taichung, Taiwan
    2. School of Medicine, Medical College, China Medical University, Taichung, Taiwan
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  • Kang-Hsu Lin MD,

    1. Neuroscience Laboratory, Department of Neurology, China Medical University Hospital, Taichung, Taiwan
    2. School of Medicine, Medical College, China Medical University, Taichung, Taiwan
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  • Jui-Cheng Chen MD,

    1. Neuroscience Laboratory, Department of Neurology, China Medical University Hospital, Taichung, Taiwan
    2. School of Medicine, Medical College, China Medical University, Taichung, Taiwan
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  • Yi-Ting Hsu MD

    Corresponding author
    1. School of Medicine, Medical College, China Medical University, Taichung, Taiwan
    • Neuroscience Laboratory, Department of Neurology, China Medical University Hospital, Taichung, Taiwan
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  • Conflict of Interest: None.

Address all correspondence to Y-T. Hsu, Department of Neurology, China Medical University Hospital, Taichung 404, Taiwan.

Abstract

Sturge-Weber syndrome is known to be associated with migraine attacks and prolong aura even without cerebral infarction. We report the case of a 36-year-old woman with type III Sturge-Weber syndrome developing with prolonged left homonymous hemianopsia after an intractable migraine-like headache and becoming a permanent visual field defect at 18-month follow up. By adopting a multimodality imaging study, we suggested that the underlying mechanism of prolonged visual field defect was due to blood flow disturbance and vasogenic leakage under the leptomeningeal angioma combining with atrophy and the damaged integrity of white matter in right occipital lobe.

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