Desmoplastic infantile ganglioglioma: A questionably benign tumour

Authors


  • A Taranath MB BS, MD; A Lam MD, FRANZCR; CKF Wong MB BS, FRANZCR.

Ajay Taranath, Department of Medical Imaging, Lyell McEwin Health Service, Elizabeth Vale, South Australia 5112, Australia. Email: ajay_deepa@yahoo.com

Summary

Desmoplastic infantile ganglioglioma is a rare intracranial tumour of childhood that involves the cerebral cortex and the leptomeninges. We report two patients with desmoplastic infantile gangliogliomas and multiple cerebrospinal metastases. To our knowledge, only two similar cases have been reported in the published literature. Pathologically, this rare intracranial tumour shows glial and ganglionic differentiation, accompanied by an extreme desmoplastic reaction. These are low-grade neoplasms that are questionably benign.

Ancillary