Rapp-Hodgkin Ectodermal Dysplasia
Article first published online: 28 JUN 2008
Volume 7, Issue 2, pages 126–131, June 1990
How to Cite
Felding, I. B. and Bjdrklund, L. J. (1990), Rapp-Hodgkin Ectodermal Dysplasia. Pediatric Dermatology, 7: 126–131. doi: 10.1111/j.1525-1470.1990.tb00668.x
- Issue published online: 28 JUN 2008
- Article first published online: 28 JUN 2008
Abstract: Rapp-Hodgkin syndrome is an uncommon, autosomai dominant condition characterized by distinctive craniofacial anomalies, cleft lip or palate, poor dentition, poor hair growth, dystrophic nails, and hypohidrosis, and hypospadias in boys. Since the originai report in 1966, fewer than 20 other patients have been described. We report a new sporadic case, a 12-year-oid boy who had erythrodermia and scaling skin at birth, and later developed most of the symptoms and findings previously described.