Dr Heptulla is the recipient of the National Institute of Health grant DK065059.
An Unusual Presentation of Mastocytosis: Unilateral Swelling of the Vulva
Article first published online: 23 NOV 2005
Volume 22, Issue 6, pages 554–557, November 2005
How to Cite
Roy, J., Metry, D. W., Hicks, J., Morgan, A. J. and Heptulla, R. A. (2005), An Unusual Presentation of Mastocytosis: Unilateral Swelling of the Vulva. Pediatric Dermatology, 22: 554–557. doi: 10.1111/j.1525-1470.2005.00139.x
- Issue published online: 23 NOV 2005
- Article first published online: 23 NOV 2005
Abstract: Mastocytosis is a primary, abnormal accumulation of mast cells associated with a broad range of local and systemic symptoms. We report two female adolescents with episodic, unilateral, swelling of the labia majora that was discovered to be an unusual presentation of mastocytosis. Mastocytosis is frequently misdiagnosed because of its rarity and variable clinical presentation, which often mimics other conditions. In the appropriate setting, mastocytosis should be included in the differential diagnosis of labium majus swelling.