Multiple Nuchal Fibromas in a 2-Year-Old Without Gardner Syndrome
Version of Record online: 25 SEP 2011
© 2011 Wiley Periodicals, Inc.
Volume 28, Issue 6, pages 695–696, November/December 2011
How to Cite
LeBlanc, K. G., Wenner, M. and Davis, L. S. (2011), Multiple Nuchal Fibromas in a 2-Year-Old Without Gardner Syndrome. Pediatric Dermatology, 28: 695–696. doi: 10.1111/j.1525-1470.2011.01415.x
- Issue online: 15 NOV 2011
- Version of Record online: 25 SEP 2011
Abstract: Nuchal fibromas, uncommon benign soft tissue tumors typically arising along the posterior neck, are often associated with Gardner syndrome (GS). These tumors have rarely been reported in association with scleroderma or as secondary to trauma and diabetes. Nuchal fibromas not associated with GS have been described predominantly in men aged 30 to 50. We report a 2-year-old African American girl with multiple nuchal fibromas along the posterior aspect of her neck and upper back. Retinal examination showed no signs of congenital hypertrophy of the retinal pigment epithelium, and genetic testing for the adenomatous polyposis coli gene mutation seen in GS was negative.