Profuse Congenital Familial Milia with Absent Dermatoglyphics (Basan’s Syndrome): Description of a New Family
Article first published online: 9 SEP 2011
© 2011 Wiley Periodicals, Inc.
Volume 29, Issue 4, pages 527–529, July/August 2012
How to Cite
Luna, P. C. and Larralde, M. (2012), Profuse Congenital Familial Milia with Absent Dermatoglyphics (Basan’s Syndrome): Description of a New Family. Pediatric Dermatology, 29: 527–529. doi: 10.1111/j.1525-1470.2011.01473.x
- Issue published online: 3 JUL 2012
- Article first published online: 9 SEP 2011
Abstract: Milia are common, small, keratin-containing cysts frequently seen in all age groups. They may arise spontaneously or develop after a variety of stimuli. They can be found alone or as part of syndromes. We present a female neonate born not only with profuse facial milia, but also with acral bullae and absent dermatoglyphics. Similar features were seen in several members of her family. These findings correspond to the syndrome known as Basan’s syndrome, a rare autosomal-dominant inherited dermatosis characterized by profuse congenital milia, transient neonatal acral bullae, and absence of dermatoglyphics.