Linear Immunoglobulin A Bullous Disease of Childhood Responsive to Intravenous Immunoglobulin Monotherapy
Article first published online: 9 SEP 2011
© 2011 Wiley Periodicals, Inc.
Volume 29, Issue 4, pages 529–532, July/August 2012
How to Cite
Nanda, A., Khawaja, F., Nanda, M., Al-Sabah, H., Selim, M. K., Dvorak, R. and Alsaleh, Q. A. (2012), Linear Immunoglobulin A Bullous Disease of Childhood Responsive to Intravenous Immunoglobulin Monotherapy. Pediatric Dermatology, 29: 529–532. doi: 10.1111/j.1525-1470.2011.01475.x
- Issue published online: 3 JUL 2012
- Article first published online: 9 SEP 2011
Abstract: We report a case of linear immunoglobulin A bullous disease in a 9-year-old boy who presented with rapidly progressive severe disease and could not tolerate dapsone because of high liver enzymes within a week after a low dose of dapsone in association with an underlying fatty liver. He showed remarkable improvement with intravenous immunoglobulins used as monotherapy, with a rapid clearance and a sustained remission after stopping the treatment.