Get access

Congenital Erosive and Vesicular Dermatosis: A New Case and Review of the Literature

Authors

  • Jacob Mashiah M.D.,

    1. Service de Dermatologie, Hôpital Necker-Enfants Malades, Université Paris V-Descartes, Paris, France
    Search for more papers by this author
  • Daniel Wallach M.D.,

    1. Service de Dermatologie, Hôpital Cochin-Tarnier, Paris, France
    Search for more papers by this author
  • Stéphanie Leclerc-Mercier M.D.,

    1. Service d’Anatomie Pathologique, Hôpital Necker-Enfants Malades, Université Paris V-Descartes, Paris, France
    2. Centre de Référence des Maladies Génétiques à Expression Cutanée, Hôpital Necker-Enfants Malades, Université Paris V-Descartes, Paris, France
    Search for more papers by this author
  • Christine Bodemer M.D., Ph.D.,

    1. Service de Dermatologie, Hôpital Necker-Enfants Malades, Université Paris V-Descartes, Paris, France
    2. Centre de Référence des Maladies Génétiques à Expression Cutanée, Hôpital Necker-Enfants Malades, Université Paris V-Descartes, Paris, France
    Search for more papers by this author
  • Smaïl Hadj-Rabia M.D., Ph.D.

    1. Service de Dermatologie, Hôpital Necker-Enfants Malades, Université Paris V-Descartes, Paris, France
    2. Centre de Référence des Maladies Génétiques à Expression Cutanée, Hôpital Necker-Enfants Malades, Université Paris V-Descartes, Paris, France
    Search for more papers by this author

Address correspondence to Smaïl Hadj-Rabia, M.D., Ph.D., Service de Dermatologie, Hôpital Necker-Enfants Malades 149 rue de Sèvres 75015 Paris, France, or e-mail: smail.hadj@inserm.fr.

Abstract

Abstract:  Congenital erosive and vesicular dermatosis is a rare syndrome first described by Cohen et al in 1985. Most of the 18 cases published have been reported in premature newborns. Affected babies typically present with erosions and vesicles that tend to heal shortly after birth with reticulated scaring. We report an additional case, followed up for 5 years, in which we excluded a pathogenic mutation in the TP63 gene.

Ancillary