Type V Aplasia Cutis Congenita: Case Report, Review of the Literature, and Proposed Treatment Algorithm
Article first published online: 4 APR 2012
© 2012 Wiley Periodicals, Inc.
Volume 30, Issue 6, pages e208–e213, November/December 2013
How to Cite
Morrow, D., Schelonka, R., Krol, A., Davies, M. and Kuang, A. (2013), Type V Aplasia Cutis Congenita: Case Report, Review of the Literature, and Proposed Treatment Algorithm. Pediatric Dermatology, 30: e208–e213. doi: 10.1111/j.1525-1470.2012.01742.x
- Issue published online: 13 NOV 2013
- Article first published online: 4 APR 2012
Abstract: Aplasia cutis congenita (ACC) is the congenital absence of skin. There are a number of different classifications based on distribution and associated findings. Type V ACC is unique in that the lesions are typically symmetric and found primarily on the trunk but can also include the upper and lower extremities. Type V is associated with the loss of a monozygotic co-twin during the late first or early second trimester. Here we present an extensive case of type V ACC and a review of the literature, including a summary of treatment and outcomes. From the available literature, it appears that there is no benefit from early surgical intervention, and therefore we propose a treatment algorithm that starts with conservative management.