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Type V Aplasia Cutis Congenita: Case Report, Review of the Literature, and Proposed Treatment Algorithm


Address correspondence to Daniel Morrow, M.D., Doernbecher Neonatal Care Center, Oregon Health and Science University, 707 SW Gaines Rd, 4232 CDRC, Mail Code CDRCP, Portland, OR 97239, USA, or e-mail:


Abstract:  Aplasia cutis congenita (ACC) is the congenital absence of skin. There are a number of different classifications based on distribution and associated findings. Type V ACC is unique in that the lesions are typically symmetric and found primarily on the trunk but can also include the upper and lower extremities. Type V is associated with the loss of a monozygotic co-twin during the late first or early second trimester. Here we present an extensive case of type V ACC and a review of the literature, including a summary of treatment and outcomes. From the available literature, it appears that there is no benefit from early surgical intervention, and therefore we propose a treatment algorithm that starts with conservative management.