Abstract:  An 8-year-old boy presented to the pediatric dermatology service with an elevated, moist and vegetated pinkish mass, measuring 4 × 5 × 2 cm in diameter, located in the scrotum. The lesion has been gradually increasing in size showing a recent accelerated growth. Excisional biopsy demonstrated the histological picture of syringocystadenoma papilliferum (SCAP). The interest of this report lies in the rarity of syringocystadenoma papilliferum, its unusual presentation in the scrotum not yet reported in pediatric literature, and the importance of differential diagnoses in this location.