Eyelid myoclonia with absences (Jeavons syndrome): A well-defined idiopathic generalized epilepsy syndrome or a spectrum of photosensitive conditions?
Article first published online: 4 MAY 2009
Wiley Periodicals, Inc. © 2009 International League Against Epilepsy
Special Issue: Epilepsy Syndromes in Development
Volume 50, Issue Supplement s5, pages 15–19, May 2009
How to Cite
Striano, S., Capovilla, G., Sofia, V., Romeo, A., Rubboli, G., Striano, P. and Trenité, D. K.-N. (2009), Eyelid myoclonia with absences (Jeavons syndrome): A well-defined idiopathic generalized epilepsy syndrome or a spectrum of photosensitive conditions?. Epilepsia, 50: 15–19. doi: 10.1111/j.1528-1167.2009.02114.x
- Issue published online: 4 MAY 2009
- Article first published online: 4 MAY 2009
- Eyelid myoclonia;
- Eyelid myoclonia with absences;
Eyelid myoclonia with absences (EMA), or Jeavons syndrome, is a generalized epileptic condition clinically characterized by eyelid myoclonia (EM) with or without absences, eye closure-induced electroencephalography (EEG) paroxysms, and photosensitivity; in addition, rare tonic–clonic seizures may also occur. Although first described in 1977 and widely reported by several authors within the last few years, EMA has not been yet recognized as a definite epileptic syndrome. However, when strict criteria are applied to the diagnosis, EMA appears to be a distinctive condition that could be considered a myoclonic epileptic syndrome, with myoclonia limited to the eyelids, rather than an epileptic syndrome with absences.