Alopecia with perineural lymphocytes: a clue to linear scleroderma en coup de sabre

Authors

  • Carolyn Goh,

    1. Division of Dermatology, David Geffen School of Medicine, University of California, Los Angeles, CA, USA
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  • Asok Biswas,

    1. Dermatopathology Section, Department of Dermatology, Boston University School of Medicine, Boston, MA, USA
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  • Lynne J. Goldberg

    Corresponding author
    1. Dermatopathology Section, Department of Dermatology, Boston University School of Medicine, Boston, MA, USA
      Lynne J. Goldberg, MD
      Department of Dermatology
      Boston University School of Medicine
      609 Albany Street
      Boston, MA 02118
      Tel: +1 617 638 5574
      Fax: +1 617 638 5515
      e-mail: lynngold@bu.edu
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Lynne J. Goldberg, MD
Department of Dermatology
Boston University School of Medicine
609 Albany Street
Boston, MA 02118
Tel: +1 617 638 5574
Fax: +1 617 638 5515
e-mail: lynngold@bu.edu

Abstract

Linear scleroderma en coup de sabre (‘the stroke of the sword’) is an uncommon form of morphea with onset typically in childhood or adolescence. Involvement is usually located on the paramedian forehead and is associated with alopecia. It is microscopically indistinguishable from other forms of scleroderma. We present a 51-year-old woman who presented with alopecia and subsequently developed linear scleroderma en coup de sabre on her adjacent forehead. Histopathology revealed a strikingly perineural lymphocytic and plasmacytic infiltrate, extending deeply into the subcutis and fascia. To our knowledge, this is the first report of alopecia with perineural lymphocytic inflammation as a presenting sign of linear scleroderma en coup de sabre.

Goh C, Biswas A, Goldberg LJ. Alopecia with perineural lymphocytes: a clue to linear scleroderma en coup de sabre.

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