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Shrinking lungs syndrome, a rare manifestation of systemic lupus erythematosus

Authors

  • C. J. ALBERTO,

    1. Division of Rheumatology, Hospital de Clinicas ‘José de San Martin’, Faculty of Medicine, University of Buenos Aires, Buenos Aires, Argentina
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  • D. DIANA,

    1. Division of Rheumatology, Hospital de Clinicas ‘José de San Martin’, Faculty of Medicine, University of Buenos Aires, Buenos Aires, Argentina
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  • N. G. GUILLERMO

    1. Division of Rheumatology, Hospital de Clinicas ‘José de San Martin’, Faculty of Medicine, University of Buenos Aires, Buenos Aires, Argentina
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Dr Cavallasca Javier Alberto, División Reumatología, Hospital de Clínicas ‘José de San Martín’, Avenida Córdoba 2351 8° Piso, Código Postal 1120 AAF, Buenos Aires, Argentina
Tel.: + 54 11 59508998
Fax: + 54 11 59508998
Email: jcavallasca@yahoo.com.ar

Summary

In systemic lupus erythematosus (SLE), the respiratory system is frequently compromised. One of its uncommon manifestations is the shrinking lungs syndrome (SLS), characterised by dyspnoea, diaphragmatic elevation and a restrictive pattern in the spirometry. We report two cases affected with this rare entity. They presented with different degrees of respiratory involvement and responses to the therapy. At the same time, clinical, physiopathological, prognostic and therapeutic aspects of this syndrome are reviewed.

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