YX Kitzing MBBS; J Gallagher MBBS, FRACS; R Waugh MBBS, FRACR.
Large focal nodular hyperplasia and extrahepatic portosystemic shunt in a male patient: Multi-modality imaging features
Article first published online: 18 OCT 2011
© 2011 The Authors. Journal of Medical Imaging and Radiation Oncology © 2011 The Royal Australian and New Zealand College of Radiologists
Journal of Medical Imaging and Radiation Oncology
Volume 55, Issue 5, pages 502–505, October 2011
How to Cite
Kitzing, Y. X., Gallagher, J. and Waugh, R. (2011), Large focal nodular hyperplasia and extrahepatic portosystemic shunt in a male patient: Multi-modality imaging features. Journal of Medical Imaging and Radiation Oncology, 55: 502–505. doi: 10.1111/j.1754-9485.2011.02303.x
Conflict of interest: None.
- Issue published online: 18 OCT 2011
- Article first published online: 18 OCT 2011
- Submitted 28 February 2011; accepted 2 March 2011.
- congenital portal vein variant;
- focal nodular hyperplasia;
- gastrointestinal imaging;
- hepatobiliary imaging;
Congenital extrahepatic portocaval shunt is a rare condition that is described mostly in female patients. We report an unusual case of a young adult male patient with type 1 congenital extrahepatic portocaval shunt with associated development of a focal nodular hyperplasia on a background of regenerative nodules. With multi-slice CT utilisation, there is increased detection of portocaval malformation in asymptomatic patients. This congenital variant is clinically significant with associated development of hepatocellular lesions, hepatic dysfunction and/or encephalopathy.